Pacman Heart as a Congenital Cardiac Defect Associated with Flail Mitral Valve and a Partial form of Shone's Complex; A Case Report

Abstract:   

Partial muscular inter-ventricular septal defect (VSD) or Pacman heart is a rare congenital or occasionally acquired anomaly. Concurrent Pacman heart and Shone's complex are extremely rare and have never been reported until now. We described a 37-year-old male patient with congenital Pacman heart, flail mitral valve (FMV), and a history of multiple congenital anomalies, including subvalvular aortic stenosis, bicuspid aortic valve (AV), and coarctation of the aorta compatible with the incomplete form of Shone's complex. Cardiac surgery was not necessary to perform for this anomaly due to the absence of a left-to-right shunt through this partial defect.

Keywords: Flail mitral leaflet, Congenital heart defects, Bicuspid aortic valve