Published May 22, 2026 | Version v1
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CASE REPORT EHLER DANLOS RARE CAUSE OF PULMONARY HYPERTENSION

Authors/Creators

  • 1. 1. MD Respiratory Medicine Consultant Pulmonologist.
  • 2. 2. MD, MRCSED, FICO Consultant Vitreo-Retinal Surgeon.
  • 3. 3. Registrar of Pulmonology MBBS.
  • 4. 4. MD Ophthalmology Specialist.

Description

Ehler Danlos syndrome is an inherited disorder that affect theconnectiv e tissue,recently Ehler Danlos syndrome subdivided in different 13 to 14 types. Ehler Danlos syndrome is not a direct cause of pulmonary hypertension but association between the two condition may occur.We presented a rare case of pulmonary hypertension as first presentation of Ehler Danlos syndrome in years male who presented with progressive dyspnea.

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