Published November 30, 2023 | Version http://impactfactor.org/PDF/IJTPR/13/IJTPR,Vol13,Issue11,Article68.pdf
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A Retrospective Study Assessing the Outcome of Repair and Resection of the Occipital Encephalocele

  • 1. Consultant, Department of Neurosurgery, Kashi Neuron Multispeciality Hospital, Ramnagar, Varanasi UP, India

Description

Aim: The aim of this study was to find the outcome of repair and resection of the occipital encephalocele. Material & Methods: A retrospective study of 50 exclusively occipital encephalocele patients was conducted in between the duration of 1 year in the Department of Neurosurgery, Kashi Neuron Multispeciality Hospital, Ramnagar Varanasi UP, India. The medical records of all operated cases of occipital encephalocele were reviewed, and relevant data such as age, sex, location of encephalocele, the size of the lesion, operative method, seizure, and hydrocephalus along with postoperative complications were recorded for analysis. Results: Of 50 patients, 19 were males and 31 females. The average age of the patients at the time of presentation was 2.4 months, ranging (4 days to 1.33 years). Most of the patients 58% belonged to 3 months age followed by 24% in 3-6 months age group. All patients presented with swelling on the head just after birth. A visible mass was situated in either the occipital (supratorcular or infratorcular). Any overlying skin varied from a thick and wrinkled to a thin or shiny covering. 18 patients (36%) presented with enlarged head circumference with associated hydrocephalus and 2 patients (4%) diagnosed with Dandy–Walker cyst. 32 (4%) patients were suspected developmental delay and mental disorders. 8 (16%) patients also had seizure. 10 (20%) patients admitted with the complication of sac rupture with cerebrospinal fluid (CSF) leakage, 1 (2%) patients having rupture of sac after the admission and 1 (2%) patients admitted with the complaint of haemorrhage from the thin and shiny covering skin of the sac. Postoperatively, only 2 (4%) patients had CSF leakage from the repaired wound. 3 (6%) patients developed Hydrocephalus after the repair of protrude sac. Conclusion: Encephalocele is commonly seen in the practice of neurosurgery in the world. Modern neuroimaging, neurosurgical techniques, and neonatal neurological intensive care have greatly improved morbidity and mortality in the care of encephalocele.

Abstract (English)

Aim: The aim of this study was to find the outcome of repair and resection of the occipital encephalocele. Material & Methods: A retrospective study of 50 exclusively occipital encephalocele patients was conducted in between the duration of 1 year in the Department of Neurosurgery, Kashi Neuron Multispeciality Hospital, Ramnagar Varanasi UP, India. The medical records of all operated cases of occipital encephalocele were reviewed, and relevant data such as age, sex, location of encephalocele, the size of the lesion, operative method, seizure, and hydrocephalus along with postoperative complications were recorded for analysis. Results: Of 50 patients, 19 were males and 31 females. The average age of the patients at the time of presentation was 2.4 months, ranging (4 days to 1.33 years). Most of the patients 58% belonged to 3 months age followed by 24% in 3-6 months age group. All patients presented with swelling on the head just after birth. A visible mass was situated in either the occipital (supratorcular or infratorcular). Any overlying skin varied from a thick and wrinkled to a thin or shiny covering. 18 patients (36%) presented with enlarged head circumference with associated hydrocephalus and 2 patients (4%) diagnosed with Dandy–Walker cyst. 32 (4%) patients were suspected developmental delay and mental disorders. 8 (16%) patients also had seizure. 10 (20%) patients admitted with the complication of sac rupture with cerebrospinal fluid (CSF) leakage, 1 (2%) patients having rupture of sac after the admission and 1 (2%) patients admitted with the complaint of haemorrhage from the thin and shiny covering skin of the sac. Postoperatively, only 2 (4%) patients had CSF leakage from the repaired wound. 3 (6%) patients developed Hydrocephalus after the repair of protrude sac. Conclusion: Encephalocele is commonly seen in the practice of neurosurgery in the world. Modern neuroimaging, neurosurgical techniques, and neonatal neurological intensive care have greatly improved morbidity and mortality in the care of encephalocele.

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Dates

Accepted
2023-11-28

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