Published September 6, 2023
| Version v1
Journal article
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HEMOPHILIA ACQUIRED AS A CAUSE OF SEVERE BLEEDING WITH NEED FOR ICU ADMISSION
Authors/Creators
- 1. Hospital Ortopédico e Medicina Especializada – HOME, Brasília-DF
- 2. Faculdades Integradas do Planalto Central – FACIPLAC, Brasília-DF
- 3. Faculdade Católica de Brasília – UCB, Brasília-DF
- 4. Centro Universitário de Brasília – CEUB, Brasília-DF
- 5. Faculdade Anhanguera de Brasília – FAB, Brasília-DF
- 6. Centro Universitário de Brasília – CEUB, Brasília-DF, Universidade de Brasília – UnB, Brasília-DF
Description
Acquired hemophilia is a rare autoimmune disease caused by depletion of coagulation factor VIII. Its incidence is higher in the elderly, there is no predominance by sex, except in women of childbearing age where there is a higher prevalence of cases. It can develop associated with Systemic Lupus Erythematosus, rheumatoid arthritis, lymphoproliferative diseases, mostly are of idiopathic causes. The goal of treatment is to eliminate the inhibitors through pulse therapy with corticosteroids and treat bleeding with the use of bypass agents.