Published June 1, 2020 | Version v1
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A Clinical and Optical Coherence Tomography Study of Coloboma in a Tertiary Health Care Centre of Uttar Pradesh

  • 1. Department of Ophthalmology, Maharani Laxmi Bai Medical College, Jhansi, Uttar Pradesh, India, *Consultant, Radiodiagnosis, Fortis Hospital, Delhi

Description

This prospective research aimed to study the clinico-etiological features of patients with coloboma, consisted of 124 eyes 
of 80 patients with coloboma. Demographic and clinical data included age at presentation, gender and parental consanguinity. The 
best-corrected visual acuity was measured with a Snellen chart or Teller chart where possible. The presence of associated ocular 
anomalies and history of prophylactic laser photocoagulation was recorded. Standard Domain Optical Coherence Tomography 
(SDOCT) was done in cooperative patients. Mean age was 11.8± 2.25 years (1 month  to 25 years). Parental consanguinity was 
documented in 7(8.75%) of the patients. 44 (55%) patients had bilateral olobomata and 36 (45%) had unilateral involvement. 
Among 80 patients, 25 (31.25%) cases had anterior colobomas, 31 (38.75%) cases had posterior involvement and 24(30%) cases 
had both anterior and posterior colobomas. Concurrent ocular anomalies were microphthalmia (32 cases, 40%), amblyopia (24 
cases, 30%), strabismus (12 cases, 15%), cataract (10 cases, 12.5%), microcornea (9 cases, 11.25%), and nystagmus (13 cases, 
16.25%). OCT in 11 cases showed a “Y-shaped” retina with a fusion of retinal layers and abrupt transition zone between the normal 
retina into the intercalary membrane (ICM) at the level of the coloboma was seen in 9 cases. Coloboma accounts for 3-11% of 
blindness  in  children  worldwide.  Early  onset  visual  loss  have  profound  consequences  on  a  child's  socio-psychological 
development. Timely diagnosis of coloboma, needful information to the parents regarding the disorder/ anomaly and visual 
rehabilitation of such subjects should be a priority. Genetic counselling may provide a pivotal role.

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References

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