Published March 10, 2020 | Version v1

A rare case report of multiple and large, small bowel neuroendocrine tumours in a 50 year old lady

  • 1. Professor and Head, Department of General Surgery, GMC Aurangabad, India
  • 2. Junior resident, Department of General Surgery, GMC Aurangabad, India

Description

Abstract

Small intestinal neuroendocrine tumors are the most common type of neuroendocrine tumors and small bowel neoplasms. The clinical presentation varies from asymptomatic incidentally detected localized lesions to lethal metastatic disease with carcinoid syndrome.

A 50 year old lady presented with chief complaints of lump in upper abdomen associated with dull aching pain for 3 months. Cect scan was suggestive of a probable gastrointestinal stromal tumour for which patient underwent elective laparotomy. Postoperatively on the basis of histopathology a diagnosis of neuroendocrine tumor was made and confirmed by immunohistochemistry. Approximately 90% of duodenal NET’s are not associated with a clinical syndrome. It is a rare diagnosis with incidence of 0.5/100,000.

Patients with well differentiated tumours diagnosed in early stage have a good prognosis with an 85% overall 5year survival rate.

Notes

International Journal of Clinical and Medical Cases (ISSN:2517-7346)

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References

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