Data set from Bernardini A, Camporeale A, Pieroni M, Pieruzzi F, Figliozzi S, Lusardi P, Spada M, Mignani R, Burlina A, Carubbi F, Battaglia Y, Graziani F, Pica S, Tondi L, Chow K, Boveri S, Olivotto I, Lombardi M. Atrial Dysfunction Assessed by Cardiac Magnetic Resonance as an Early Marker of Fabry Cardiomyopathy. JACC Cardiovasc Imaging. 2020 Oct;13(10):2262-2264. doi: 10.1016/j.jcmg.2020.05.011. Epub 2020 Jun 17. PMID: 32563647.
- Andrea Bernardini1
- Antonia Camporeale2
- Maurizio Pieroni3
- Federico Pieruzzi4
- Stefano Figliozzi5
- Paola Lusardi6
- Marco Spada7
- Renzo Mignani8
- Alessandro Burlina9
- Francesca Carubbi10
- Yuri Battaglia11
- Francesca Graziani12
- Silvia Pica13
- Lara Tondi14
- Kristian Chow15
- Sara Boveri16
- Ike Olivotto17
- Massimo Lombardi18
- 1. Department of Arrhythmology, IRCCS Policlinico San Donato, Piazza Edmondo Malan 1, San Donato Milanese, 20097 Milan, Italy.
- 2. Multimodality Cardiac Imaging Section, IRCCS Policlinico San Donato, Milan, Italy.
- 3. Cardiovascular Department, San Donato Hospital, Arezzo, Italy.
- 4. Nephrology and Dialysis Unit, Department of Medicine and Surgery, University of Milano Bicocca, ASST-Monza San Gerardo Hospital, Monza, Italy.
- 5. Department of Cardiovascular Medicine, Humanitas Clinical and Research Center - IRCCS, Milan, Italy.
- 6. Department of Cardiology, Humanitas Hospital, Torino, Italy.
- 7. Department of Pediatrics, University of Torino, AOU Città della Salute e della Scienza di Torino, Torino, Italy.
- 8. Department of Nephrology and Dialysis, Infermi Hospital, AUSL Romagna, Rimini, Italy.
- 9. Neurological Unit, St. Bassiano Hospital, Bassano del Grappa, Italy.
- 10. Metabolic Medicine Unit, University of Modena and Reggio Emilia, Modena, Italy.
- 11. Nephrology and Dialysis Unit, University-Hospital St. Anna, Ferrara, Italy.
- 12. Department of Cardiovascular and Thoracic Sciences, Fondazione Policlinico Universitario A. Gemelli IRCCS, Rome, Italy.
- 13. Multimodality Cardiac Imaging Section, IRCCS Policlinico San Donato, San Donato Milanese, Milan, Italy.
- 14. Department of Multimodality Cardiovascular Imaging, IRCCS Policlinico San Donato, San Donato Milanese, Italy.
- 15. Department of Community Health Sciences, University of Calgary, Calgary, AB.
- 16. Scientific Directorate, IRCCS Policlinico San Donato, Milan, Italy.
- 17. Department of Life and Environmental Sciences, Polytechnic University of Marche, via Brecce Bianche, 60131 Ancona, Italy.
- 18. Department of Cardiovascular Sciences, Fondazione Policlinico Universitario A. Gemelli IRCCS, Università Cattolica del Sacro Cuore, Largo A. Gemelli, 8-00168 Rome, Italy.
Description
Data set from the article Bernardini A, Camporeale A, Pieroni M, Pieruzzi F, Figliozzi S, Lusardi P, Spada M, Mignani R, Burlina A, Carubbi F, Battaglia Y, Graziani F, Pica S, Tondi L, Chow K, Boveri S, Olivotto I, Lombardi M. Atrial Dysfunction Assessed by Cardiac Magnetic Resonance as an Early Marker of Fabry Cardiomyopathy. JACC Cardiovasc Imaging. 2020 Oct;13(10):2262-2264. doi: 10.1016/j.jcmg.2020.05.011. Epub 2020 Jun 17. PMID: 32563647.
Brief introduction
Anderson-Fabry disease (AFD) cardiomyopathy is characterized by glycosphingolipid (Gb3) storage in all cellular components, with consequent left ventricular hypertrophy (LVH). Gb3 accumulation also involves atrial myocytes (1), ultimately leading to left atrial (LA) enlargement and reduced atrial compliance. Cardiac magnetic resonance (CMR) plays an important role in the assessment of the severity of Fabry cardiomyopathy. CMR feature tracking (CMR-FT) specifically allows the assessment of myocardial strain from cine images
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