Heyde Syndrome: A Case Report and Review of Literature

The triad of AV Malformations in the GI tract, Aortic Stenosis and Von Willebrand Disease is known to us as the Heyde Syndrome. We present the case of a 72 years old male patient who presented with Heyde Syndrome Secondary to Aortic Stenosis (Mean gradient of 36) with Proximal Jejunal Arteriovenous malformation- Dieulafoy lesion, seen on Push enteroscopy and capsule endoscopy. The patient had a  porcelain Aorta visible on CT and MRI. A Transcutaneous Aortic Valve Replacement-TAVR was planned to replace the Aortic Valve. Edwardes S3 Prosthetic Size 26 Valve was used. A follow up Echocardiography 3 months after the surgery shows that there is no Aortic Valve stenosis. The patient also underwent a follow up Anterograde Double Balloon Enteroscopy which shows that the AVMs had diminished and are currently non bleeding. The high risk patient with Heyde Syndrome and a Porcelain Aorta recovered with the use of TAVR.