Published April 1, 2019 | Version v1
Journal article Open

A rare case of Zinner syndrome

Authors/Creators

  • 1. Junior Resident, Department of Radiodiagnosis, Goa Medical College
  • 2. Professor and Head, Department of Radiodiagnosis, Goa Medical College

Description

The present article reports a case of Zinner syndrome which consists of a triad of mesonephric duct abnormalities presenting as a seminal vesicle cyst, ipsilateral renal agenesis and ejaculatory duct obstruction in a 37-year-old male undergoing an infertility workup. There are also rare associated anomalies noted in this case. The presence of an unusual associated anomaly resulted in the rare presentation of this case.  A limited review of  literature is also presented.

Files

A Rare Case of Zinner Syndrome.pdf

Files (775.7 kB)

Name Size
md5:5fa80ed369dace8e49e8fc42c7c9123a
775.7 kB Preview Download

Additional details

References

  • Zinner A. Ein fall von intravesikaler Samenblasenzyste. Wien Med Wochenschr. 1914;64(605):e9.
  • Shah S, Patel R, Sinha R, Harris M. Zinner syndrome: an unusual cause of bladder outflow obstruction. BJR|case reports. 2017;3(2):20160094. doi:10.1259/bjrcr.20160094
  • Hannema SE, Hughes IA. Regulation of Wolffian Duct Development. Horm Res Paediatr. 2007;67(3):142-151. doi:10.1159/000096644
  • Gianna P, Giuseppe PG. Mayer-Rokitansky-Küster-Hauser syndrome and the Zinner syndrome, female and male malformation of reproductive system: Are two separate entities. J Chinese Clin Med. 2007;2:11.
  • van den Ouden D, Blom JH, Bangma C, de Spiegeleer AH. Diagnosis and management of seminal vesicle cysts associated with ipsilateral renal agenesis: a pooled analysis of 52 cases. Eur Urol. 1998;33(5):433-440.
  • Heaney J, Pfister R, Meares E. Giant cyst of the seminal vesicle with renal agenesis. Am J Roentgenol. 1987;149(1):139-140. doi:10.2214/ajr.149.1.139
  • Okada Y, Tanaka H, Takeuchi H, Yoshida O. Papillary adenocarcinoma in a seminal vesicle cyst associated with ipsilateral renal agenesis: a case report. J Urol. 1992;148(5):1543-1545.
  • Eldefrawy A, Arianayagam M, Kanagarajah P, Acosta K, Manoharan M. Anomalies of the inferior vena cava and renal veins and implications for renal surgery. Cent Eur J Urol. 2011;64(1):4-8. doi:10.5173/ceju.2011.01.art1
  • Adeniji AO. Congenital seminal vesicle cyst with ipsilateral renal agenesis, vascular anomalies and intestinal malrotation. Appl Radiol. 2009;38(10):40A-40C.
  • Trigaux JP, Van Beers B, Delchambre F. Male genital tract malformations associated with ipsilateral renal agenesis: sonographic findings. J Clin Ultrasound. 1991;19(1):3-10.
  • Livingston L, Larsen CR. Seminal Vesicle Cyst with Ipsilateral Renal Agenesis. Am J Roentgenol. 2000;175(1):177-180. doi:10.2214/ajr.175.1.1750177
  • MURPHY JO, POWER RE, AKHTAR M, TORREGGIANI WC, McDERMOTT TED, THORNHILL JA. Magnetic Resonance Imaging in the Diagnosis of Seminal Vesicle Cysts and Associated Anomalies. J Urol. 2003;170(6):2386-2386. doi:10.1097/01.ju.0000088339.38119.4
  • King BF, Hattery RR, Lieber MM, Berquist TH, Williamson B, Hartman GW. Congenital cystic disease of the seminal vesicle. Radiology. 1991;178(1):207-211. doi:10.1148/radiology.178.1.1984306
  • Shebel HM, Farg HM, Kolokythas O, El-Diasty T. Cysts of the Lower Male Genitourinary Tract: Embryologic and Anatomic Considerations and Differential Diagnosis. RadioGraphics. 2013;33(4):1125-1143. doi:10.1148/rg.334125129

Subjects

Radiology
http://id.loc.gov/authorities/subjects/sh85110774.html
Medical radiology
http://id.loc.gov/authorities/subjects/sh85110777.html