Published December 22, 2017 | Version v1

CASE REPORT: PSUEDO-THROMBOTIC THROMBOCYTOPENIC PURPRA AND COBALAMINE DEFICIENCY.

  • 1. Department of pediatrics, Hematology Oncology, King Fahd Armed Forces Hospital, Jeddah, Saudi Arabia.

Description

Pseudothrombotic microangiopathy is thrombocytopenia, anemia and schistocytosis caused by Cobalamine deficiency. It could be easily misdiagnosed as microangiopathic hemolytic anemia. Evaluation of lactate dehydrogenase, reticulocyte count, peripheral blood smear, platelet count, cobalamine and homocysteine level are crucial for differentiating pseudothrombotic microangiopathy from a true microangiopathic hemolytic anemia. A case of pseudothrombotic microangiopathy due to severe vitamin B12 deficiency is presented.

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