case_images: PMC4319291_01
case_images: Depicts the macules and areas of hyperpigmentation along with severe ocular abnormalities
case_images: EJD-9-145-g001.jpg
case_images: PMC4319291_01_EJD-9-145-g001.jpg
case_images: F1
case_images: The patient had multiple, small, dark brown colored lentigines appeared as tanned pigmented macules, on the face, varying in size and shape with areas of depigmentation in association with significant visual impairment [Figure 1].
case_images: Reveals the perioral scarring due to actinic chilitis
case_images: EJD-9-145-g002.jpg
case_images: PMC4319291_01_EJD-9-145-g002.jpg
case_images: F2
case_images: The lips were red with areas of bleeding and crusted along with perioral scarring that leads to limited mouth opening along with actinic cheilitis [Figure 2].
case_images: Intraoral view revealed dark brown and gray pigmentation, poor oral hygiene, periodontitis and enamel hypoplasia upper central incisor
case_images: EJD-9-145-g003.jpg
case_images: PMC4319291_01_EJD-9-145-g003.jpg
case_images: F3
case_images: She had protrusion of maxillary anterior teeth and Class II division 2 malocclusion [Figure 3].
case_images: Illustrates the generalized bone loss and spacing
case_images: EJD-9-145-g004.jpg
case_images: PMC4319291_01_EJD-9-145-g004.jpg
case_images: F4
case_images: Orthopantomogram reveals the severe generalized bone loss along with spacing [Figure 4].