case_images: PMC10589413_01
case_images: clubbed cyanotic fingers and toes
case_images: PAMJ-45-154-g001.jpg
case_images: PMC10589413_01_PAMJ-45-154-g001.jpg
case_images: F1
case_images: Fingers and toes were clubbed and cyanotic with intact pulses (Figure 1).
case_images: chest X-ray showing right aortic arch
case_images: PAMJ-45-154-g002.jpg
case_images: PMC10589413_01_PAMJ-45-154-g002.jpg
case_images: F2
case_images: Chest radiography revealed a right aortic arch (RAA) (Figure 2).
case_images: parasternal long-axis echocardiographic view showing ascending aorta overriding the interventricular septum
case_images: PAMJ-45-154-g003.jpg
case_images: PMC10589413_01_PAMJ-45-154-g003.jpg
case_images: F3
case_images: A two-dimensional echocardiogram revealed moderate right atrial enlargement, right ventricular enlargement and hypertrophy with impaired systolic function, large perimembranous outlet ventricular septal defect (VSD) of 21 mm and an overriding aorta (Figure 3).
case_images: continuous wave Doppler across right ventricular outflow tract in parasternal short-axis view showing a gradient of 75 mmHg
case_images: PAMJ-45-154-g004.jpg
case_images: PMC10589413_01_PAMJ-45-154-g004.jpg
case_images: F4
case_images: Doppler examination revealed an infundibular obstruction with a right ventricular outflow tract (RVOT) gradient of 75 mmHg (Figure 4).
case_images: 3D contrast-enhanced computed tomography image demonstrating hypoplastic main pulmonary artery
case_images: PAMJ-45-154-g005.jpg
case_images: PMC10589413_01_PAMJ-45-154-g005.jpg
case_images: F5
case_images: It also showed RAA, VSD with overriding aorta, RVOT narrowing with RVH and aortopulmonary collateral channels (Figure 5, Figure 6).
case_images: 3D contrast-enhanced CT image demonstrating ascending aorta dilation with right aortic arch
case_images: PAMJ-45-154-g006.jpg
case_images: PMC10589413_01_PAMJ-45-154-g006.jpg
case_images: F6
case_images: It also showed RAA, VSD with overriding aorta, RVOT narrowing with RVH and aortopulmonary collateral channels (Figure 5, Figure 6).