case_images: PMC11650254_01
case_images: A: Dark mucocutaneous pigmented macules over the lower lip and buccal mucosa. B. Thyroid swelling.
case_images: gr1.jpg
case_images: PMC11650254_01_gr1.jpg
case_images: f0005
case_images: Additionally, the patient had multiple black pigmented lesions over the lower lip (Fig. 1A) since childhood and midline neck swelling (Fig. 1B) for 2 years.
case_images: CECT Abdomen-Axial Section showing target sign (A: red circle) and jejunojejunal intussusception (B: red circle).. CECT: Contrast-Enhanced Computed Tomography.
case_images: gr2.jpg
case_images: PMC11650254_01_gr2.jpg
case_images: f0010
case_images: Contrast-enhanced computed tomography (CECT) revealed multiple polypoidal masses in the 2nd, 3rd, and 4th parts of the duodenum, the largest measuring 23*21 mm, and 3 jejunal polyps, the largest measuring 41*22 mm (Fig. 2), with jejuno-jejunal intussusception at 3 sites (Fig. 3, Fig. 4).
case_images: CECT Abdomen-Axial Section showing enhancing soft tissue polypoidal lesion at duodenum (A: red arrow) and at jejunum (B: red arrow).. CECT: Contrast-Enhanced Computed Tomography.
case_images: gr4.jpg
case_images: PMC11650254_01_gr4.jpg
case_images: f0020
case_images: Contrast-enhanced computed tomography (CECT) revealed multiple polypoidal masses in the 2nd, 3rd, and 4th parts of the duodenum, the largest measuring 23*21 mm, and 3 jejunal polyps, the largest measuring 41*22 mm (Fig. 2), with jejuno-jejunal intussusception at 3 sites (Fig. 3, Fig. 4).
case_images: A: Jejuno-jejunal intussusception (black arrow) B: Serosal indentation (black arrow) due to polyp serving as a lead point.
case_images: gr5.jpg
case_images: PMC11650254_01_gr5.jpg
case_images: f0025
case_images: Treitz) (Fig. 5A) with pedunculated polyps served as a lead point (Fig. 5B), which was revealed on enterotomy. There were multiple polyps (3 larger polyps and multiple smaller polyps) in the jejunum spanning about 20 cm of the jejunum (Fig. 6), so segmental jejunal resection was done, followed by side-to-side jejuno-jejunal stapled anastomosis.
case_images: Resected specimen of jejunum showing multiple pedunculated polyps (white arrow) in its lumen.
case_images: gr6.jpg
case_images: PMC11650254_01_gr6.jpg
case_images: f0030
case_images: Treitz) (Fig. 5A) with pedunculated polyps served as a lead point (Fig. 5B), which was revealed on enterotomy. There were multiple polyps (3 larger polyps and multiple smaller polyps) in the jejunum spanning about 20 cm of the jejunum (Fig. 6), so segmental jejunal resection was done, followed by side-to-side jejuno-jejunal stapled anastomosis.
case_images: Histopathological examination showing papillary villous architecture with tree-like arborization of compact smooth muscle bundle surrounded by goblet cells. A: 40x magnification; B: 100x magnification.
case_images: gr7.jpg
case_images: PMC11650254_01_gr7.jpg
case_images: f0035
case_images: Histopathological examination of the specimen revealed a hamartomatous polyp without a feature of dysplasia (Fig. 7), characteristic of PJS.