case_images: PMC6837811_01
case_images: Lateral radiograph of the skull shows normal bone density with wormian bones in the lambdoid suture (hollow arrow), prognathism and supernumerary teeth (white arrow). Patient is wearing dental prosthesis.
case_images: SAJR-22-1326-g001.jpg
case_images: PMC6837811_01_SAJR-22-1326-g001.jpg
case_images: F0001
case_images: A lateral radiograph of the skull (Figure 1) showed normal bone density, wormian bones (white arrow), mandibular prognathism and supernumerary teeth.
case_images: Water's view for paranasal sinuses shows an open metopic suture (hollow arrow), aplastic frontal sinuses, hypoplastic maxillary sinuses (white arrows) and underpneumatised mastoids.
case_images: SAJR-22-1326-g002.jpg
case_images: PMC6837811_01_SAJR-22-1326-g002.jpg
case_images: F0002
case_images: Radiographs of the PNS sinuses (Figure 2) revealed an open metopic suture, aplasia of the frontal sinuses, hypoplasia of the maxillary sinuses and underpneumatised mastoids.
case_images: Postero-anterior radiograph of the upper chest shows aplasia of lateral two-thirds of both clavicles (white arrows) and a bell-shaped thorax.
case_images: SAJR-22-1326-g003.jpg
case_images: PMC6837811_01_SAJR-22-1326-g003.jpg
case_images: F0003
case_images: Radiographs of the shoulders (Figure 3) demonstrated aplasia of the lateral two-thirds of both clavicles and a bell-shaped thorax.
case_images: Coronal section of computed tomography-paranasal region shows supernumerary unerupted teeth, a deviated nasal septum, hypoplastic maxillary sinuses and a high-arched palate.
case_images: SAJR-22-1326-g004.jpg
case_images: PMC6837811_01_SAJR-22-1326-g004.jpg
case_images: F0004
case_images: Non-contrast CT of the PNS revealed normal bone density, multiple supernumerary teeth, a deviated nasal septum and a high-arched palate (Figure 4), a dysplastic clivus which was flexed with convexity towards the endocranium (Figure 5), an open metopic suture and sclerotic mastoids (Figure 6).
case_images: Sagittal-section computed tomography scan shows a dysplastic clivus with its flexion deformity and convexity towards the endocranium (arrow).
case_images: SAJR-22-1326-g005.jpg
case_images: PMC6837811_01_SAJR-22-1326-g005.jpg
case_images: F0005
case_images: Non-contrast CT of the PNS revealed normal bone density, multiple supernumerary teeth, a deviated nasal septum and a high-arched palate (Figure 4), a dysplastic clivus which was flexed with convexity towards the endocranium (Figure 5), an open metopic suture and sclerotic mastoids (Figure 6).
case_images: Axial-computed tomography section at the level of skull base (a) shows under-pneumatised mastoids, non-pneumatised sphenoid sinuses and superiorly (b) shows an open metopic suture (curved arrow).
case_images: SAJR-22-1326-g006.jpg
case_images: PMC6837811_01_SAJR-22-1326-g006.jpg
case_images: F0006
case_images: Non-contrast CT of the PNS revealed normal bone density, multiple supernumerary teeth, a deviated nasal septum and a high-arched palate (Figure 4), a dysplastic clivus which was flexed with convexity towards the endocranium (Figure 5), an open metopic suture and sclerotic mastoids (Figure 6).