case_images: PMC3271301_01
case_images: Gross findings. (A) Micrognathia, (B) Clubbing fingers, (C) Slim extremities compared with trunk.
case_images: jkms-27-225-g001.jpg
case_images: PMC3271301_01_jkms-27-225-g001.jpg
case_images: F1
case_images: Physical examination revealed micrognathia (Fig. 1A), clubbing fingers (Fig. 1B), and slim extremities compared with trunk (Fig. 1C).
case_images: Hyperpigmented, telangiectatic, and atrophic changes on the skin. (A) Trunk. (B) both axillae.
case_images: jkms-27-225-g002.jpg
case_images: PMC3271301_01_jkms-27-225-g002.jpg
case_images: F2
case_images: Dermatologic examination showed generalized hyperpigmented, telangiectatic, and atrophic changes with accentuation on both axillae (Fig. 2), antecubital, and popliteal fossae.
case_images: Linear brownish hyperkeratotic and sclerosing band on the skin. (A) Popliteal fossa. (B) Antecubital fossa.
case_images: jkms-27-225-g003.jpg
case_images: PMC3271301_01_jkms-27-225-g003.jpg
case_images: F3
case_images: Linear hyperkeratotic and sclerotic bands were found on the both antecubital and popliteal fossae (Fig. 3).
case_images: Histopathological findings of the skin. (A) Increased melanin pigments in the basal layer and sclerotic changes and telangiectasia in the upper dermis (H&E, x 40). (B) Fragmentations of elastic fibers in the dermis (Elastic stain, x 200).
case_images: jkms-27-225-g004.jpg
case_images: PMC3271301_01_jkms-27-225-g004.jpg
case_images: F4
case_images: Histopathologic finding revealed increased melanin pigments in the basal layer and sclerotic changes and telangiectasia in the upper dermis (Fig. 4A). The fragmentations of elastic fibers in the dermis were noted in elastic stain (Fig. 4B) consistent with a diagnosis of HSP.