case_images: PMC9062908_01
case_images: Anteroposterior radiograph of the patient depicting collapse of lumbar vertebrae and a coronal shift of around 4 cm to the left side.
case_images: SNI-13-136-g001.jpg
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case_images: F1
case_images: X-rays revealed a lumbar spine deformity characterized by L2-L4 vertebral lysis [Figures 1 and 2].
case_images: Plain lateral radiograph of the patient depicting gross lumbar kyphosis. There is a loss of multiple lumbar vertebrae architecture evident in the radiographs. The overall lumbar lordosis is around 30  but there is gross instability due to loss of multiple lumbar vertebral bodies. The sagittal vertebral axis is shifted around "-3 cm."
case_images: SNI-13-136-g002.jpg
case_images: PMC9062908_01_SNI-13-136-g002.jpg
case_images: F2
case_images: X-rays revealed a lumbar spine deformity characterized by L2-L4 vertebral lysis [Figures 1 and 2].
case_images: A magnetic resonance imaging T2-weighted sagittal image showing hyperintense signals in the lumbar vertebrae in both anterior and posterior elements of the vertebrae. It justifies and correlates with the chylous fluid found peroperative.
case_images: SNI-13-136-g003.jpg
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case_images: F3
case_images: In addition, the CT/myelo-CT demonstrated dilated cysts within the L2-L4 posterior elements [Figures 3-6].
case_images: Sagittal reconstruction of computed tomographic scan of the patient showing multiple lytic defects in the body of the lumbar vertebra and the lumbar kyphosis.
case_images: SNI-13-136-g004.jpg
case_images: PMC9062908_01_SNI-13-136-g004.jpg
case_images: F4
case_images: In addition, the CT/myelo-CT demonstrated dilated cysts within the L2-L4 posterior elements [Figures 3-6].
case_images: Coronal magnetic resonance myelogram showing a partial myelo-block along with fluid intensity in the anterior and posterior elements of the vertebra.
case_images: SNI-13-136-g005.jpg
case_images: PMC9062908_01_SNI-13-136-g005.jpg
case_images: F5
case_images: In addition, the CT/myelo-CT demonstrated dilated cysts within the L2-L4 posterior elements [Figures 3-6].
case_images: Sagittal MR myelogram suggestive of a partial myelogram block at the kyphotic apex at L2-L3.
case_images: SNI-13-136-g006.jpg
case_images: PMC9062908_01_SNI-13-136-g006.jpg
case_images: F6
case_images: In addition, the CT/myelo-CT demonstrated dilated cysts within the L2-L4 posterior elements [Figures 3-6].
case_images: Intraoperative photograph of the patient showing the four-rod construct with domino connectors and placement of copious quantities of bone grafts.
case_images: SNI-13-136-g007.jpg
case_images: PMC9062908_01_SNI-13-136-g007.jpg
case_images: F7
case_images: A spinopelvic fusion was performed from T5 to T12 through the L5/S2 levels using anchors to the pelvis and S2 alar/iliac screws (i.e., supplemented with a four-rod cobalt chrome construct and cross-links) [Figures 7-9].
case_images: Postoperative anteroposterior radiograph demonstrating that coronal tilt is well corrected to within 1 cm of the midline after posterior stabilization with multiple point anchors and multirod construct.
case_images: SNI-13-136-g008.jpg
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case_images: F8
case_images: A spinopelvic fusion was performed from T5 to T12 through the L5/S2 levels using anchors to the pelvis and S2 alar/iliac screws (i.e., supplemented with a four-rod cobalt chrome construct and cross-links) [Figures 7-9].
case_images: Postoperative lateral radiographs showing good correction of lumbar kyphosis. The sagittal vertebral axis is corrected to "+2 cm."
case_images: SNI-13-136-g009.jpg
case_images: PMC9062908_01_SNI-13-136-g009.jpg
case_images: F9
case_images: A spinopelvic fusion was performed from T5 to T12 through the L5/S2 levels using anchors to the pelvis and S2 alar/iliac screws (i.e., supplemented with a four-rod cobalt chrome construct and cross-links) [Figures 7-9].
case_images: Follow-up anteroposterior radiograph at 4 years depicting maintained correction and no implant failure. There is no further progression of disease to other segments.
case_images: SNI-13-136-g010.jpg
case_images: PMC9062908_01_SNI-13-136-g010.jpg
case_images: F10
case_images: Both the CT and MR studies continue to confirm remission of GSD; the CT scan shows bony bridging/ fusion/stability, while the MRI demonstrates no new vertebral bony reformation [Figures 10-12].
case_images: Follow-up lateral radiograph showing maintained alignment.
case_images: SNI-13-136-g011.jpg
case_images: PMC9062908_01_SNI-13-136-g011.jpg
case_images: F11
case_images: Both the CT and MR studies continue to confirm remission of GSD; the CT scan shows bony bridging/ fusion/stability, while the MRI demonstrates no new vertebral bony reformation [Figures 10-12].
case_images: 3-D computed tomographic reconstruction showing good posterior and posterolateral bony fusion along the reconstruction.
case_images: SNI-13-136-g012.jpg
case_images: PMC9062908_01_SNI-13-136-g012.jpg
case_images: F12
case_images: Both the CT and MR studies continue to confirm remission of GSD; the CT scan shows bony bridging/ fusion/stability, while the MRI demonstrates no new vertebral bony reformation [Figures 10-12].