case_images: PMC11333362_01
case_images: Imaging results for Case 1. (A) Chest x-ray: The cardiac silhouette was full, with increased and blurred pulmonary vascular markings in both lungs. (B-D) Axial and coronal view of CTA: The superior limbic band of the septum secundum is absent (*), the left superior and inferior pulmonary veins drain into the left atrium, and the right superior and inferior pulmonary veins drain into the anatomical right atrium (accessory atrium). A localized defect () is visible between the ectopic septum primum ( ). (E,F) Volume rendering (VR): The right atrium was enlarged, the right pulmonary vein drained into the right atrium, and the left pulmonary vein drained into the left atrium. The left superior vena cava drained into the right atrium through the anterior edge of the left pulmonary vein and the posterior edge of the left atrium, with a thickened and enlarged confluence area. (G) Doppler echocardiography: A septum secundum defect () was observed, with the septum primum shifted to the left ( ), resulting in the abnormal drainage of the right pulmonary veins into the right atrium.
case_images: fped-12-1436608-g001.jpg
case_images: PMC11333362_01_fped-12-1436608-g001.jpg
case_images: F1
case_images: See Figure 1 for details.
case_images: Imaging results for Case 2. (A) Chest x-ray: The heart was enlarged with a rounded and blunt apex. The pulmonary vascular markings were increased and coarse, accompanied by flocculent shadows. (B-D) Axial and coronal view of CTA: The right atrium was enlarged. The left superior and inferior pulmonary veins drained into the left atrium, while the right superior and inferior pulmonary veins drained into the anatomical right atrium (accessory atrium). A localized defect () was visible between the ectopic septum primum ( ), and the superior limbic band of the septum secundum was absent (*). (E) Doppler echocardiography: The right atrium was dilated, the atrial septum was abnormally deviated to the left and small in size ( ), the superior limbic band of the septum secundum was absent (*), and the right pulmonary vein drained into the anatomical right atrium.
case_images: fped-12-1436608-g002.jpg
case_images: PMC11333362_01_fped-12-1436608-g002.jpg
case_images: F2
case_images: See Figure 2 for details.