case_images: PMC3262527_01
case_images: Xanthoma on elbow skin in, (a) an atheroma protruding into the aortic lumen in (b) (red star).
case_images: CARDIOLOGY2011-804767.001.jpg
case_images: PMC3262527_01_CARDIOLOGY2011-804767.001.jpg
case_images: fig1
case_images: On inspection, the xanthomas on her elbow and knee were rather evident (Figure 1(a)). TEE also showed a diffuse narrowing of the aorta from annular level to the descending thoracic aorta (Figure 1(b)). The diameters of the aorta were measured as 1.1, 1.4, and 1.5 cm at the levels of the aortic annulus, sinotubular junction, and ascending aorta, respectively, (body surface area was 1.56 m2).
case_images: MR angiogram showing diffuse narrowing of the entire aorta.
case_images: CARDIOLOGY2011-804767.002.jpg
case_images: PMC3262527_01_CARDIOLOGY2011-804767.002.jpg
case_images: fig2
case_images: Magnetic resonance angiography confirmed the diffuse narrowing of the entire aorta (Figure 2).
case_images: Critical ostial and mid portion stenosis of the right coronary artery and a moderate ostial stenosis of the LMCA on coronary angiography.
case_images: CARDIOLOGY2011-804767.003.jpg
case_images: PMC3262527_01_CARDIOLOGY2011-804767.003.jpg
case_images: fig3
case_images: Coronary angiograms showed a critical ostial stenosis of the right coronary artery and a moderate ostial narrowing of the left main coronary artery (LMCA) (Figure 3).