case_images: PMC5958583_01
case_images: (a) Patient with dry, scaly skin seen all over the body. (b) Skin biopsy showing orthokeratosis, diminished granular layer with mild perivascular lymphocytic infiltrate in superficial dermis
case_images: JFMPC-7-261-g001.jpg
case_images: PMC5958583_01_JFMPC-7-261-g001.jpg
case_images: F1
case_images: On examination, skin was dry scaly all over the body [Figure 1a] with similar skin manifestation in his first cousins. Skin biopsy confirmed the diagnosis of IV [Figure 1b].