case_images: PMC11198933_01
case_images: Facial dysmorphism, short stature, broad chest, wide-spaced nipple (black arrow), pectus excavatum (orange arrow), webbed neck (red arrow)
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case_images: With the abovementioned dysmorphism, he was suspected to be a Noonan phenotype [Figure 1] and sent to our institute for cardiac evaluation.
case_images: Electrocardiogram - Northwest axis deviation, poor R wave progression in left precordial leads
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case_images: His electrocardiogram revealed a heart rate of 75 beats/min, sinus rhythm, northwest axis deviation, and poor R wave progression in the left precordial leads [Figure 2].
case_images: Significantly dilated left coronary artery system. LMCA: Left main coronary artery, LAD: Left anterior descending, LCx: Left circumflex
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case_images: The right coronary system was not well visualized [Figure 3].
case_images: Computed tomography coronary angiography - Spider view showing dilated left anterior descending and right coronary artery. LAD: Left anterior descending, LCx: Left circumflex, RCA: Right coronary artery
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case_images: It revealed aneurysmal dilatation with a beaded appearance of bilateral coronary arteries in their proximal course [Figures 4-6].
case_images: Computed tomography - Coronary angiography showing aneurysmal left (a) and right-sided coronary arterial system (b)
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case_images: It revealed aneurysmal dilatation with a beaded appearance of bilateral coronary arteries in their proximal course [Figures 4-6].
case_images: Three-dimensional multiplanar reconstruction reconstruction showing dilated coronary arterial system. LAD: Left anterior descending, LCx: Left circumflex, RCA: Right coronary artery, PDA: Posterior descending artery, RV: Right ventricular, LV: Left ventricular, RA: Right atrial, LA: Left atrial
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case_images: It revealed aneurysmal dilatation with a beaded appearance of bilateral coronary arteries in their proximal course [Figures 4-6].