case_images: PMC7085362_01
case_images: Pure tone audiometry of case 1 before surgery (left ear). (a) Low-tone sensorineural hearing loss (21.3 dB). (b) Hearing had once gotten better (13.8 dB). (c) Exacerbations and remissions (46.3 dB). (d) The hearing suddenly worse (66.3 dB).
case_images: CRIOT2020-9476915.001.jpg
case_images: PMC7085362_01_CRIOT2020-9476915.001.jpg
case_images: fig1
case_images: A 61-year-old woman with blocked ear and low-tone sensorineural hearing loss (21.3 dB) (Figure 1(a)) in the left ear was admitted to the hospital in 2007. Her hearing had improved of the left (13.8 dB) (Figure 1(b)) after treatment with dexamethasone. There had been gradual sensorineural hearing loss of the left from 2010 to 2013 (approximately 46.3 dB) (Figure 1(c)). She felt sudden worsening of sensorineural hearing loss of the left with blocked ear and tinnitus like a stream in 2015 and hearing in the left ear declined suddenly (66.3 dB) (Figure 1(d)) to almost the level of the right ear without apparent cause.
case_images: HRCT. The fusion of the vestibules and the lateral semicircular canals. (a) Right ear. (b) Left ear.
case_images: CRIOT2020-9476915.002.jpg
case_images: PMC7085362_01_CRIOT2020-9476915.002.jpg
case_images: fig2
case_images: High-resolution computed tomography (HRCT) showed hypoplasty of the lateral semicircular canals along with fusion of the vestibules and the lateral semicircular canals (Figures 2(a) and 2(b)), but there was no pneumolabyrinth.
case_images: 3D fast imaging employing steady-state acquisition-cycled phases (FIESTA-C) magnetic resonance imaging (MRI). The fusion of the vestibules and the lateral semicircular canals.
case_images: CRIOT2020-9476915.003.jpg
case_images: PMC7085362_01_CRIOT2020-9476915.003.jpg
case_images: fig3
case_images: FIESTA-C providing high signal from CSF based on T2/T1 contrast showed no vestibular schwannomas. FIESTA-C used in the 3D mode provided the fusion of the vestibules and the lateral semicircular canals in more detail (Figure 3).