case_images: PMC8100182_01
case_images: PMC8100182_02
case_images: High resolution chest CT showing diffuse thickening of the interlobular septae (white arrows) in the right lung.
case_images: fped-09-657473-g0001.jpg
case_images: PMC8100182_02_fped-09-657473-g0001.jpg
case_images: F1
case_images: A high resolution chest CT revealed diffuse, extensive thickening of the interlobular septae on the right leading to a suspicion for unilateral lymphangiectasia (Figure 1).
case_images: Wedge resection of right lower lobe. (A) Hematoxylin-Eosin stain showing thickened pleura and septum containing increased number of markedly dilated lymphatic channels. (B) Trichrome stain showing fibrosis (blue) in the pleura and septum. (C) Immunostain staining nuclei red confirming lymphatic origin of endothelium of dilated pleural and septal vessels.
case_images: fped-09-657473-g0002.jpg
case_images: PMC8100182_02_fped-09-657473-g0002.jpg
case_images: F2
case_images: The patient underwent a thoracoscopic lung biopsy at the age of 2 which identified pleural and septal fibrosis with dilated lymphatics consistent with pulmonary lymphangiectasia (Figure 2).
case_images: PMC8100182_03