case_images: PMC4153236_01
case_images: Patient with typical spinal muscular atrophy type 1 using continuous noninvasive ventilatory support via nasal interface.
case_images: Tanaffos-12-070-g001.jpg
case_images: PMC4153236_01_Tanaffos-12-070-g001.jpg
case_images: F0001
case_images: Currently, at age 18, she has a VC of 120 ml (2% of normal), no measurable cough flows, and requires high span bi-level PAP continuously via nasal interfaces (Figure 1) with less than 2 minute periods free from it before respiratory distress and blood gas derangement necessitate return to ventilatory support.