case_images: PMC4005212_01
case_images: (a) A chest X-ray with right sided pneumothorax. (b) A chest X-ray of the same patient after 2 days with intercostal tube in situ and fully expanded right lung
case_images: JFMPC-3-86-g001.jpg
case_images: PMC4005212_01_JFMPC-3-86-g001.jpg
case_images: F1
case_images: A repeat chest X-ray was done, which showed fully expanded right lung with bilateral cystic changes [Figure 1a and b].
case_images: (a) X-ray chest of the same patient with second episode of right sided pneumothorax. (b) Chest X-ray of the same patient with intercostal tube in situ and a partially expanded lung
case_images: JFMPC-3-86-g002.jpg
case_images: PMC4005212_01_JFMPC-3-86-g002.jpg
case_images: F2
case_images: Her examination findings were consistent with right sided pneumothorax, which was confirmed on X-ray chest [Figure 2a]. This time even after 72 h, patient did not have complete lung expansion and continued to have air leak [Figure 2b].
case_images: High resolution computed tomography scan of the chest showing diffuse thin-walled cystic changes of the pulmonary parenchyma and right-sided pneumothorax with intercostal tube in situ, all findings characteristic of lymphangiomyomatosis
case_images: JFMPC-3-86-g003.jpg
case_images: PMC4005212_01_JFMPC-3-86-g003.jpg
case_images: F3
case_images: HRCT was done [Figure 3] which showed multiple well-defined diffusely distributed variable sized and irregular shaped cystic areas in bilateral lung fields present in both intraparenchymal and subpleural location with few nodules and increased linear interstitial markings with right pneumothorax, which were suggestive of cystic lung disease, probably LAM.