case_images: PMC8553436_01
case_images: Cafe au lait spots or coffee with milk spots; it consists in hyperpigmented lesions that may vary in color from light brown to dark brown.
case_images: CRIS2021-2868966.001.jpg
case_images: PMC8553436_01_CRIS2021-2868966.001.jpg
case_images: fig1
case_images: However, we observed brownish skin lesions, also known as cafe au lait spots or coffee with milk spots that consists in hyperpigmented lesions that may vary in color from light brown to dark brown (Figure 1).
case_images: Neurofibromas on the anterior thigh.
case_images: CRIS2021-2868966.002.jpg
case_images: PMC8553436_01_CRIS2021-2868966.002.jpg
case_images: fig2
case_images: These lesions correspond to neurofibromas (Figure 2).
case_images: Abdominal ultrasound showing heterogeneous retroperitoneal nodular lesion, vascularized using color Doppler in presence of multiple partitions.
case_images: CRIS2021-2868966.003.jpg
case_images: PMC8553436_01_CRIS2021-2868966.003.jpg
case_images: fig3
case_images: Abdominal CT enhanced scan shows a 5 cm exophytic duodenum mass, revealing a stromal tumor.
case_images: CRIS2021-2868966.004.jpg
case_images: PMC8553436_01_CRIS2021-2868966.004.jpg
case_images: fig4
case_images: It does not show any reverberation or signs of locoregional extension (Figure 4).
case_images: A tumor located 7 cm from the major axis, located at D1 with exophytic lesions, of centimeter size, located at the surface of the small bowel, resembling fibroids.
case_images: CRIS2021-2868966.005.jpg
case_images: PMC8553436_01_CRIS2021-2868966.005.jpg
case_images: fig5
case_images: As a conclusion, the patient undertook a pancreaticoduodenectomy, and intraoperative exploration revealed a tumor measuring 7 cm, with a significant collateral venous circulation, located at D1 and independent of the pancreas (Figure 5).