case_images: PMC4237194_01
case_images: Pathology change of transbronchial lung biopsy (hematoxylin and eosin staining, A x 40; B x 200) showed fibrous tissue hyperplasia, inflammatory cell infiltration and histiocytic reaction in alveolar space. Chronic inflammatory cell infiltration and foamy phagocytes groups in small wall-thickened bronchioles and interstitial lung.
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case_images: fig01
case_images: The pathology change of transbronchial lung biopsy showed respiratory bronchiolitis (Fig. 1).
case_images: Electron microscopy of nasal mucosa showed cilia with the absence of both outer and inner dynein arms of the microtubules (transmission electron microscopy, 3 200 000).
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case_images: fig02
case_images: Then the absence of both outer and inner dynein arms of the microtubules was found by examination of the nasal mucosal biopsy specimen under transmission electron microscopy (Fig. 2).
case_images: Computed tomography (CT) images of the chest. (A) High-resolution computed tomography (HRCT) shows bronchiectasis and bronchiolitis, ring-shaped or ductal opacities in upper, middle and lower lungs, some of which are accompanied by small nodules. (B) Bronchiectasis involved in right middle lobe.
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case_images: Bronchiectasis mainly involved in the right middle lobe (Fig. 3).
case_images: Computed tomography (CT) images of the sinuses showed chronic maxillary sinusitis and (B) ethmoid sinusitis.
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case_images: Paranasal sinus CT showed chronic maxillary sinusitis and ethmoid sinusitis (Fig. 4).
case_images: High-resolution computed tomography (HRCT) images after 20 days of azithromycin therapy. (A) Nodular shadows were obviously attenuated, (B) but bronchiectasis did not change.
case_images: crj0008-0425-f5.jpg
case_images: PMC4237194_01_crj0008-0425-f5.jpg
case_images: fig05
case_images: Chest CT showed that nodular shadows were mildly attenuated after 2 months of azithromycin therapy, but bronchiectasis was not improved (Fig. 5).