case_images: PMC4732263_01
case_images: Axial noncontrast (a) computed tomography images shows a well-defined intraconal mass in the posterior right orbit. Postcontrast image (b) heterogenous enhancement of the lesion causing proptosis and medial displacement of optic nerve
case_images: AJNS-11-78a-g001.jpg
case_images: PMC4732263_01_AJNS-11-78a-g001.jpg
case_images: F1
case_images: Computed tomography (CT scan) revealed a well-defined intraconal mass in the posterior right orbit with postcontrast heterogenous enhancement causing proptosis and medial displacement of optic nerve [Figure 1].
case_images: Magnetic resonance sagittal images shows a retro-orbital lesion of hypointense signal on T1-weighted (a) with postcontrast T1-weighted image (b) revealing heterogenous enhancement of the lesion
case_images: AJNS-11-78a-g002.jpg
case_images: PMC4732263_01_AJNS-11-78a-g002.jpg
case_images: F2
case_images: Postcontrast T1-weighted image revealed a heterogenous enhancement of the lesion [Figure 2].
case_images: (a) Tumor revealing patternless fibroblastic proliferation and vascular channels with pericytomatous arrangement (H and E, x100) (b) spindle cells growing in a haphazard manner in a variable cellular stroma described as "patternless pattern" (H and E, x400)
case_images: AJNS-11-78a-g003.jpg
case_images: PMC4732263_01_AJNS-11-78a-g003.jpg
case_images: F3
case_images: There was no significant cellular atypia and mitosis was 1-2/10 high-power fields [Figure 3].
case_images: Tumor cells with strong and diffuse positivity to CD34 (a) but negativity for S-100 (b)
case_images: AJNS-11-78a-g004.jpg
case_images: PMC4732263_01_AJNS-11-78a-g004.jpg
case_images: F4
case_images: On immunohistochemistry, the tumor cells had strong and diffuse positivity to CD34, vimentin and bcl-2 but negativity for S-100, progesterone receptor, smooth-muscle actin (SMA), and cytokeratin [Figure 4].