case_images: PMC7403915_01
case_images: Color fundus photo of the right eye (a) and left eye (b).
case_images: CRIOPM2020-8897394.001.jpg
case_images: PMC7403915_01_CRIOPM2020-8897394.001.jpg
case_images: fig1
case_images: Fundoscopy revealed 0.5+ vitreous cell without haze in both eyes (OU); healthy appearing optic nerves OU; and extensive, serpentine peripapillary chorioretinal scarring OU with extension into the macula (Figures 1(a) and 1(b)).
case_images: Composite images of the right eye: color fundus photo (a); fundus autofluorescence (b); magnified superficial en face OCT reflectance slab demonstrating ORT margins (c); and magnified color-coded OCTA of superficial, deep, and choriocapillaris vessels showing dropout beyond normal-appearing retina (d). White arrows demonstrate the corresponding area which is intact on fundus photo (a) and autofluorescence (b), lies within the border of the outer retinal tubules seen on en face imaging (c), but demonstrates patchy dropout of choriocapillaris identical to adjacent areas. Of note, there is increased visibility of choriocapillaris at the legion margins, seen as yellow-coded vessels and analogous to window defect.
case_images: CRIOPM2020-8897394.002.jpg
case_images: PMC7403915_01_CRIOPM2020-8897394.002.jpg
case_images: fig2
case_images: OCT reflectance and OCTA imaging were obtained, which demonstrated severe atrophy with outer retinal tubules and patchy dropout of choriocapillaris in areas of otherwise normal-appearing retina, respectively (Figure 2). Over the next 2 months, the prednisone was slowly tapered and she continued mycophenolate mofetil 1 gram twice daily without recurrence of intraocular inflammation or activation of disease at the lesion margins.