case_images: PMC4465165_01
case_images: Transmission electron microscopy (EM) of representative nasal epithelium cilia from patient #1 with primary ciliary dyskinesia caused by demonstration of cilia lacking of inner dynein arms and ciliary abnormalities of symmetry presumably related to defects in the radial spokes.
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case_images: PMC4465165_01_40248_2015_15_Fig1_HTML.jpg
case_images: Fig1
case_images: In 2007 the nasal brushing was performed, with demonstration of 100% cilia lacking of inner dynein arm associated with axonemal disorganization in 60% of the cilia, presumably related to defects in the radial spokes (Figure 1).
case_images: PMC4465165_02
case_images: Transmission electron microscopy (EM) of representative nasal epithelium cilia from patient #2 with primary ciliary dyskinesia caused by demonstration of cilia lacking of lacking outer dynein arm.
case_images: 40248_2015_15_Fig2_HTML.jpg
case_images: PMC4465165_02_40248_2015_15_Fig2_HTML.jpg
case_images: Fig2
case_images: In 2007 the nasal brushing was performed, with demonstration of 100% cilia lacking outer dynein arm (Figure 2).
case_images: PMC4465165_03
case_images: Transmission electron microscopy (EM) of representative nasal epithelium cilia from patient #3 with primary ciliary dyskinesia caused by demonstration of cilia lacking of lacking outer dynein arm.
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case_images: PMC4465165_03_40248_2015_15_Fig3_HTML.jpg
case_images: Fig3
case_images: In 2007 the nasal brushing was performed, showing all examined cilia lacking outer dynein arm (Figure 3).
case_images: CT-scan performed in patient #3 during hospitalization for pneumonia in lower left lobe.
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case_images: PMC4465165_03_40248_2015_15_Fig4_HTML.jpg
case_images: Fig4
case_images: He was hospitalized for pneumonia to the lower left lobe as reported in the chest CT scan done on September 18, 2013 (Figure 4).
case_images: PMC4465165_04
case_images: Transmission electron microscopy (EM) of representative nasal epithelium cilia from patient #4 with primary ciliary dyskinesia caused by demonstration of cilia lacking of lacking outer dynein arms.
case_images: 40248_2015_15_Fig5_HTML.jpg
case_images: PMC4465165_04_40248_2015_15_Fig5_HTML.jpg
case_images: Fig5
case_images: In 2008 the nasal brushing was performed, showing the absence of outer dynein arms in all the ciliary sections (Figure 5).
case_images: CT-scan performed in patient #4 during hospitalization for pneumonia in upper left lobe.
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case_images: PMC4465165_04_40248_2015_15_Fig6_HTML.jpg
case_images: Fig6
case_images: She had more chest CT scans, and the last one was done in 2013 (Figure 6).
case_images: PMC4465165_05
case_images: Transmission electron microscopy (EM) of representative nasal epithelium cilia from patient #5 with primary ciliary dyskinesia caused by demonstration of cilia lacking of lacking outer dynein arm.
case_images: 40248_2015_15_Fig7_HTML.jpg
case_images: PMC4465165_05_40248_2015_15_Fig7_HTML.jpg
case_images: Fig7
case_images: In 2008 the nasal brushing was performed, with demonstration of 100% of cilia lacking outer dynein arms (Figure 7).
case_images: PMC4465165_06
case_images: Transmission electron microscopy (EM) of representative nasal epithelium cilia from patient #6 with demonstration of cilia with presence of both dynein arms but abnormalities in number and disposition of outer microtubular pair.
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case_images: PMC4465165_06_40248_2015_15_Fig8_HTML.jpg
case_images: Fig8
case_images: About 60% of cilia displayed aberrant number and/or localization of central or peripheral microtubules (Figure 8).
case_images: Patient #6, the cilia were asymmetric, some of them lacking of central pair. Basal bodies showed an atypical distribution.
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case_images: PMC4465165_06_40248_2015_15_Fig9_HTML.jpg
case_images: Fig9
case_images: Basal bodies showed an atypical distribution (Figure 9).
case_images: PMC4465165_07
case_images: Transmission electron microscopy (EM) of representative nasal epithelium cilia from patients #7 with demonstration of 50% normal ciliated cells. In the remaining 50% ciliated cells axonemes lacking both dynein arms were found.
case_images: 40248_2015_15_Fig10_HTML.jpg
case_images: PMC4465165_07_40248_2015_15_Fig10_HTML.jpg
case_images: Fig10
case_images: In the remaining 50% ciliated cells axonemes lacking both dynein arms were observed (Figure 10).
case_images: PMC4465165_08
case_images: Transmission electron microscopy (EM) of representative nasal epithelium cilia from patients #8 with primary ciliary dyskinesia caused by lacking of inner dynein arms.
case_images: 40248_2015_15_Fig11_HTML.jpg
case_images: PMC4465165_08_40248_2015_15_Fig11_HTML.jpg
case_images: Fig11
case_images: In 2008 the nasal brushing was performed, with 100% of the cilia lacking inner dynein arms (Figure 11).