case_images: PMC5904780_01
case_images: Neurofibromas and cafe au lait spots on the skin.
case_images: CRIU2018-2302918.001.jpg
case_images: PMC5904780_01_CRIU2018-2302918.001.jpg
case_images: fig1
case_images: We detected common skin nodules on his whole body, particularly on his torso in physical examination (Figure 1).
case_images: Spindle cell lesion in resection specimen (H&E stain, 100x). No atypia, left inset (H&E stain, 200x). Positive expression with smooth muscle actin immunohistochemistry, right inset (100x).
case_images: CRIU2018-2302918.002.jpg
case_images: PMC5904780_01_CRIU2018-2302918.002.jpg
case_images: fig2
case_images: Immunohistochemistry was positive for smooth muscle actin (SMA) and vimentin (Figure 2).
case_images: Mass on the left wall of bladder and ureter dilatation. The arrow shows the dilatation of ureter.
case_images: CRIU2018-2302918.003.jpg
case_images: PMC5904780_01_CRIU2018-2302918.003.jpg
case_images: fig3
case_images: CT revealed grade 3 left hydroureteronephrosis and a tumor formation of 6 x 3.5 cm extending from the left lateral wall to the anterior wall of the bladder (Figure 3).