case_images: PMC10982349_01
case_images: (A,B) Fetal MRI performed at 34 weeks of gestation showing a right renal fossa occupied by a 60 mm x 30 mm multinodular solid mass with intermediate signal intensity on T2. (C) Postnatal abdominal MRI showing a lobulated heterogeneous mass in the right renal fossa 81 mm x 58 mm.
case_images: fped-12-1334544-g001.jpg
case_images: PMC10982349_01_fped-12-1334544-g001.jpg
case_images: F1
case_images: At 34 WG, a fetal magnetic resonance imaging (MRI) scan was performed and confirmed the presence of a solid multinodular right renal mass of 6 cm with a normal contralateral kidney and no other associated congenital malformations (Figures 1A,B). It was well limited to the kidney with no evidence of enlarged lymph nodes (Figure 1C).
case_images: (A,B) Pathology (H&E) of the kidney tumor showing pupillary structures supported by triphasic neoplastic proliferation comprising immature glomerular and tubular structures and immature small round blue cells. (C) Background renal parenchyma showing microcystic dilated tubules, strangled by concentric layers of spindled mesenchymal cells.
case_images: fped-12-1334544-g002.jpg
case_images: PMC10982349_01_fped-12-1334544-g002.jpg
case_images: F2
case_images: A pathology study revealed a well-circumscribed and encapsulated tumoral proliferation that was limited to the kidney (Figure 2).
case_images: Isolated lateralized hemihypertrophy of the right lower limb. (A) At 1 month of age. (B) At 4 years of age.
case_images: fped-12-1334544-g003.jpg
case_images: PMC10982349_01_fped-12-1334544-g003.jpg
case_images: F3
case_images: At 1 month of age, the infant developed an isolated right lower limb hemihypertrophy without skin staining (Figure 3).