case_images: PMC8010253_01
case_images: Abdominal enhanced computed tomography angiography (CTA). A. Bilateral renal veins are enlarged and thickened. B. The right branch of the portal vein is extremely thin, with a diameter of 1.2 mm. The left branch and the junction are not apparent in the images. C. The inferior vena cava and pelvic vein are remarkably dilated, and the widest point is 41 mm.
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case_images: PMC8010253_01_fped-09-647364-g0001.jpg
case_images: F1
case_images: As revealed on abdominal enhanced computed tomography angiography (CTA), the intrahepatic PV was extremely thin, the external hepatic PV communicated with the body vein, and the pelvic vein was significantly dilated (Figure 1).
case_images: Cranial magnetic resonance imaging. Arachnoid cysts of occipital (the arrow underlying) and left middle cranial fossa (the arrow above) had been detected.
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case_images: PMC8010253_01_fped-09-647364-g0002.jpg
case_images: F2
case_images: Arachnoid cysts of the occipital (5.69 x 2.58 cm) and left middle cranial fossa (3.85 x 1.03 cm) were detected on abdominal enhanced computed (MRI), while patchy abnormal signal shadows were apparent on both sides of the globus pallidus and cerebral peduncle (Figure 2).
case_images: Light microscopy and electron microscopy images of kidney involvement. Hematoxylin and eosin stain (A) and Jones silver stain (B) are light microscopy images. The mesangial and endothelial cells exhibit diffuse proliferation. The capillaries are narrow, the capillary loop slightly thickened, and a "dual-track" sign can be partially observed. In addition, epithelial cells of the renal tubule exhibit granule denaturation while there was no obvious atrophy of renal tubules and no interstitial fibrosis. (C) Electron microscopy image. Electron dense deposits were observed in the mesangial and deputy mesangial regions, as well as a small amount of electron-dense deposit in the subepithelium.
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case_images: PMC8010253_01_fped-09-647364-g0003.jpg
case_images: F3
case_images: Under optical microscopy, mesangial cells and endothelial cells exhibited diffuse proliferation, the capillaries were narrow, the capillary loop was slightly thickened, and a "dual-track" sign could be partially observed (Figures 3A,B). Simultaneously, electron-dense deposits were observed in mesangial and deputy mesangial regions, as well as a small amount of electron-dense deposit in the subepithelium (Figure 3C).