case_images: PMC11338914_01
case_images: (A, B) MRI scanning revealed an abnormal signal nodular shadow in the pineal region.
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case_images: PMC11338914_01_fonc-14-1392540-g001.jpg
case_images: f1
case_images: Compression of the third ventricle and the cerebral aqueduct was observed, leading to obstructive hydrocephalus in the supratentorial ventricles, suggestive of a neoplastic lesion ( Figures 1 ,  2 ).
case_images: (A-C) Enhanced MRI showed marked heterogeneous enhancement.
case_images: fonc-14-1392540-g002.jpg
case_images: PMC11338914_01_fonc-14-1392540-g002.jpg
case_images: f2
case_images: Compression of the third ventricle and the cerebral aqueduct was observed, leading to obstructive hydrocephalus in the supratentorial ventricles, suggestive of a neoplastic lesion ( Figures 1 ,  2 ).
case_images: Histological morphology. (A, B) The cells were rich and grew in a solid, sheet-like manner with alternating densities. (C, D) The tumor cells were short spindle-shaped and oval, without a specific arrangement pattern. (E, F) The background showed staghorn vessels and collagen.
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case_images: f3
case_images: The stroma contained staghorn blood vessels and collagen ( Figure 3 ).
case_images: Immunohistochemistry. Tumor cells positive for STAT6, CD34, Bcl-2, CD99.
case_images: fonc-14-1392540-g004.jpg
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case_images: f4
case_images: Immunohistochemistry demonstrated the tumor cells to be positive for CD34, CD99, STAT6, and BCL-2 ( Figure 4 ), while negative for S-100, CD45, P-CK, CD56 (focally positive), Sy, GFAP, SALL4, OCT3/4, and Desmin.
case_images: (A-C) Postoperative follow-up magnetic resonance imaging.
case_images: fonc-14-1392540-g005.jpg
case_images: PMC11338914_01_fonc-14-1392540-g005.jpg
case_images: f5
case_images: SFTs are graded from grade 1 to grade 3 (CNS WHO grades 1 to 3), with grade 1 characterized by sparse tumor cells, absence of mitotic figures and necrosis, and a stroma often containing hyalinized collagen fibers; grade 2 by increased tumor cell density, possible atypia, and visible mitotic figures (<5 per 10 HPF); and grade 3 by abundant tumor cells, high density, marked atypia, and visible mitotic figures (>5 per 10 HPF), with necrosis. Long-term follow-up(4 months after surgery) with imaging studies showed no evidence of tumor recurrence or metastasis ( Figure 5 ).