case_images: PMC6251460_01
case_images: Multimodal images of the right eye.. Notes: Color photo (A) shows peri-macular discoloration caused by RPE alterations; Red-free image (B) with consonant changes in RPE; (C) FAF with clumps of hypo-autofluorescence around the posterior pole and tiny halo of hyper-autofluorescence around the fovea. IVFA (D, E) demarcates the window defects, as well as the spiculated pigments, with impaired edges of the fovea. (F, G) OCTA locate zones of non-perfusion in both outer retina and choriocapillaris. OCT sections (H, I) show flat clivus, folds on the outer limiting membrane, discontinuity of the Henle and ellipsoidal layers, with unequal choroidal thickness.. Abbreviations: FAF, fundus autofluorescence; IVFA, intravenous fluorescein angiography; OCT-A, OCT angiography; RPE, retinal pigment epithelium.
case_images: imcrj-11-339Fig1.jpg
case_images: PMC6251460_01_imcrj-11-339Fig1.jpg
case_images: f1-imcrj-11-339
case_images: OCT angiography (OCT-A) showed foveal thickness as being RE 255 mum and LE 321 mum; presence of bilateral epiretinal membrane, more significant in LE, with disappearance of clivus and formation of folds; bilateral sectoral discontinuities in the ellipsoid zones. OCT-A identified points of non-perfusion in the outer retina and central choriocapillaris and peri-discs, without corresponding to pigments (DRI Swept Source OCT Triton Plus; Topcon, Tokyo, Japan) (Figures 1 and 2).
case_images: Multimodal images of the left eye.. Notes: Color photo (A) and red-free image (B) show peri-macular discoloration and greater visibility of the pigment alterations below the macula. Superficial micro-hemorrhage (A, arrow). FAF (C) shows the numerous islands of hypo-autofluorescence around the macula, with the fovea being limited by a hyper-autofluorescent halo (C, black arrow). IVFA (D-F) highlights the diffuse hypofluorescence of the disc and bordering the zones of pigment epithelium and/or choriocapillaris atrophy. OCTA shows small zones of nonperfusion (G, H, arrows) especially in outer retina and choriocapillaris. OCT section (I) shows the surface folds (arrow).. Abbreviations: FAF, fundus autofluorescence; IVFA, intravenous fluorescein angiography; OCT-A, OCT angiography; OCT, optical coherence tomography.
case_images: imcrj-11-339Fig2.jpg
case_images: PMC6251460_01_imcrj-11-339Fig2.jpg
case_images: f2-imcrj-11-339
case_images: OCT angiography (OCT-A) showed foveal thickness as being RE 255 mum and LE 321 mum; presence of bilateral epiretinal membrane, more significant in LE, with disappearance of clivus and formation of folds; bilateral sectoral discontinuities in the ellipsoid zones. OCT-A identified points of non-perfusion in the outer retina and central choriocapillaris and peri-discs, without corresponding to pigments (DRI Swept Source OCT Triton Plus; Topcon, Tokyo, Japan) (Figures 1 and 2).