AARS AARS2 ABCB11 ABCB4 ABCB7 ABCD4 ACAD9 ACADM ACADVL ACO2 ACSF3 ADCK3 CABC1 COQ8 ADCK4 AFG3L2 AGK AGL AIFM1 ALAS2 ALDOA ALDOB ALG1 ALG11 ALG13 ALG2 ALG3 ALG6 ALG9 AMACR APOPT1 APTX ARG1 ASL ASS1 ATP5A1 ATP5E ATP7B ATP8B1 ATPAF2 ATP12 AUH B4GALT1 BCKDHA BCKDHB BCS1L BOLA3 C10ORF2 C12ORF65 C19orf12 CA5A CARS2 CHKB CISD2 CLPB COA5 C2ORF64 COA6 COASY COG4 COG5 COG6 COG7 COG8 COQ2 COQ4 COQ6 COQ9 COX10 COX14 C12ORF62 COX15 COX20 FAM36A COX4I2 COX6A1 COX6B1 COX7B CPS1 CPT1A CPT2 CYC1 DARS DARS2 DBT DDHD1 DDHD2 DDOST DGUOK DLAT DLD DMGDH DNA2 DNAJC19 DNM1L DNM2 DOLK DPAGT1 DPM1 DPM3 EARS2 ECHS1 ELAC2 ENO3 ETFA ETFB ETFDH ETHE1 FAH FARS2 FASTKD2 FBP1 FBXL4 FDX1L FH FLAD1 FOXRED1 G6PC GAA GAMT GARS GATM GBE1 GCDH GFER GFM1 EFG1 GFM2 GLRX5 GMPPA GSS GTPBP3 GYG1 GYG2 GYS1 GYS2 HADHA HADHB HARS2 HCFC1 HIBCH HLCS HMGCL HMGCS2 HSD17B10 HSPD1 IARS2 IBA57 ISCA2 ISCU IVD LAMP2 LARS LARS2 LDHA LIAS LIPT1 LMBRD1 LRPPRC LYRM4 LYRM7 MARS MARS2 MCCC1 MCCC2 MCEE MFF MFN2 MGAT2 MGME1 MICU1 MLYCD MMAA MMAB MMACHC MMADHC C2ORF25 MOGS MPC1 BRP44L MPDU1 MPI MPV17 MRPL12 MRPL3 MRPL44 MRPS16 MRPS22 MRPS7 MTFMT MTO1 MTPAP MTR MTRR MUT NADK2 NAGS NARS2 NDUFA1 NDUFA10 NDUFA11 NDUFA12 NDUFA2 NDUFA4 NDUFA9 NDUFAF1 NDUFAF2 NDUFAF3 C3ORF60 NDUFAF4 C6ORF66 NDUFAF5 NDUFAF6 NDUFAF7 C2ORF56 NDUFB3 NDUFB9 NDUFS1 NDUFS2 NDUFS3 NDUFS4 NDUFS6 NDUFS7 NDUFS8 NDUFV1 NDUFV2 NFS1 NFU1 NGLY1 NR2F1 NUBPL OPA1 OPA3 OTC PARS2 PC PCCA PCCB PDHA1 PDHB PDHX PDP1 PDSS1 PDSS2 PET100 PFKM PGAM2 PGM1 PHKA1 PHKA2 PHKB PHKG2 PMM2 PNPT1 POLG POLG2 PRKAG2 PRPS1 PTRH2 PUS1 PYGM QARS RANBP2 RARS RARS2 REEP1 C2ORF23 RFT1 RMND1 RRM2B SARS2 SCO1 SCO2 SDHA SDHAF1 SERAC1 SFXN4 SLC19A2 SLC19A3 SLC22A5 SLC25A1 SLC25A13 SLC25A15 SLC25A19 SLC25A20 SLC25A22 SLC25A3 PHC SLC25A38 SLC25A4 SLC2A2 SLC35A1 SLC35A2 SLC35C1 SLC37A4 SLC6A8 SLC7A7 SPAST SPG7 SPTLC1 SRD5A3 SSR4 STT3A STT3B STXBP1 SUCLA2 SUCLG1 SURF1 TACO1 TARS2 TAZ TIMM8A TK2 TMEM126A TMEM165 TMEM70 TPK1 TRIT1 TRMU TRNT1 TSFM TTC19 TUFM TYMP UQCC2 UQCC3 UQCRB UQCRC2 UQCRQ VARS2 WDR45 WFS1 YARS2