ENTRY       hsa00650                    Pathway
NAME        Butanoate metabolism - Homo sapiens (human)
CLASS       Metabolism; Carbohydrate metabolism
PATHWAY_MAP hsa00650  Butanoate metabolism
MODULE      hsa_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:hsa00650]
DBLINKS     GO: 0019605
ORGANISM    Homo sapiens (human) [GN:hsa]
GENE        39  ACAT2; acetyl-CoA acetyltransferase 2 [KO:K00626] [EC:2.3.1.9]
            38  ACAT1; acetyl-CoA acetyltransferase 1 [KO:K00626] [EC:2.3.1.9]
            3033  HADH; hydroxyacyl-CoA dehydrogenase [KO:K00022] [EC:1.1.1.35]
            3030  HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha [KO:K07515] [EC:4.2.1.17 1.1.1.211]
            1962  EHHADH; enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
            1892  ECHS1; enoyl-CoA hydratase, short chain 1 [KO:K07511] [EC:4.2.1.17]
            35  ACADS; acyl-CoA dehydrogenase short chain [KO:K00248] [EC:1.3.8.1]
            116285  ACSM1; acyl-CoA synthetase medium chain family member 1 [KO:K23756] [EC:6.2.1.2]
            123876  ACSM2A; acyl-CoA synthetase medium chain family member 2A [KO:K01896] [EC:6.2.1.2]
            341392  ACSM4; acyl-CoA synthetase medium chain family member 4 [KO:K01896] [EC:6.2.1.2]
            54988  ACSM5; acyl-CoA synthetase medium chain family member 5 [KO:K01896] [EC:6.2.1.2]
            6296  ACSM3; acyl-CoA synthetase medium chain family member 3 [KO:K01896] [EC:6.2.1.2]
            348158  ACSM2B; acyl-CoA synthetase medium chain family member 2B [KO:K01896] [EC:6.2.1.2]
            142827  ACSM6; acyl-CoA synthetase medium chain family member 6 [KO:K01896] [EC:6.2.1.2]
            79944  L2HGDH; L-2-hydroxyglutarate dehydrogenase [KO:K00109] [EC:1.1.99.2]
            2571  GAD1; glutamate decarboxylase 1 [KO:K01580] [EC:4.1.1.15]
            2572  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
            18  ABAT; 4-aminobutyrate aminotransferase [KO:K13524] [EC:2.6.1.19 2.6.1.22]
            7915  ALDH5A1; aldehyde dehydrogenase 5 family member A1 [KO:K00139] [EC:1.2.1.24]
            3157  HMGCS1; 3-hydroxy-3-methylglutaryl-CoA synthase 1 [KO:K01641] [EC:2.3.3.10]
            3158  HMGCS2; 3-hydroxy-3-methylglutaryl-CoA synthase 2 [KO:K01641] [EC:2.3.3.10]
            3155  HMGCL; 3-hydroxy-3-methylglutaryl-CoA lyase [KO:K01640] [EC:4.1.3.4]
            54511  HMGCLL1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase like 1 [KO:K01640] [EC:4.1.3.4]
            5019  OXCT1; 3-oxoacid CoA-transferase 1 [KO:K01027] [EC:2.8.3.5]
            64064  OXCT2; 3-oxoacid CoA-transferase 2 [KO:K01027] [EC:2.8.3.5]
            65985  AACS; acetoacetyl-CoA synthetase [KO:K01907] [EC:6.2.1.16]
            622  BDH1; 3-hydroxybutyrate dehydrogenase 1 [KO:K00019] [EC:1.1.1.30]
COMPOUND    C00022  Pyruvate
            C00024  Acetyl-CoA
            C00025  L-Glutamate
            C00026  2-Oxoglutarate
            C00042  Succinate
            C00091  Succinyl-CoA
            C00122  Fumarate
            C00132  Methanol
            C00136  Butanoyl-CoA
            C00164  Acetoacetate
            C00207  Acetone
            C00232  Succinate semialdehyde
            C00246  Butanoic acid
            C00332  Acetoacetyl-CoA
            C00334  4-Aminobutanoate
            C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
            C00497  (R)-Malate
            C00741  Diacetyl
            C00810  (R)-Acetoin
            C00877  Crotonoyl-CoA
            C00989  4-Hydroxybutanoic acid
            C01089  (R)-3-Hydroxybutanoate
            C01144  (S)-3-Hydroxybutanoyl-CoA
            C01384  Maleic acid
            C01412  Butanal
            C01769  (S)-Acetoin
            C01845  Propan-2-ol
            C02331  Vinylacetyl-CoA
            C02411  Glutaconyl-1-CoA
            C02527  Butanoylphosphate
            C02630  2-Hydroxyglutarate
            C03044  (R,R)-Butane-2,3-diol
            C03046  (S,S)-Butane-2,3-diol
            C03058  2-Hydroxyglutaryl-CoA
            C03561  (R)-3-Hydroxybutanoyl-CoA
            C04546  (R)-3-((R)-3-Hydroxybutanoyloxy)butanoate
            C06010  (S)-2-Acetolactate
            C06142  1-Butanol
            C06143  Poly-beta-hydroxybutyrate
            C06144  3-Butynoate
            C06145  3-Butyn-1-al
            C06146  3-Butyn-1-ol
            C11062  4-Hydroxybutyryl-CoA
            C17530  Methyl acetate
            C20657  meso-2,3-Butanediol
            C20783  Propane
            C21390  Butane
REL_PATHWAY hsa00010  Glycolysis / Gluconeogenesis
            hsa00020  Citrate cycle (TCA cycle)
            hsa00250  Alanine, aspartate and glutamate metabolism
            hsa00330  Arginine and proline metabolism
            hsa00620  Pyruvate metabolism
            hsa00750  Vitamin B6 metabolism
KO_PATHWAY  ko00650
///
