ENTRY       hsa00604                    Pathway
NAME        Glycosphingolipid biosynthesis - ganglio series - Homo sapiens (human)
CLASS       Metabolism; Glycan biosynthesis and metabolism
PATHWAY_MAP hsa00604  Glycosphingolipid biosynthesis - ganglio series
MODULE      hsa_M00069  Glycosphingolipid biosynthesis, ganglio series, LacCer => GT3 [PATH:hsa00604]
DBLINKS     GO: 0001574
ORGANISM    Homo sapiens (human) [GN:hsa]
GENE        2583  B4GALNT1; beta-1,4-N-acetyl-galactosaminyltransferase 1 [KO:K00725] [EC:2.4.1.92]
            8705  B3GALT4; beta-1,3-galactosyltransferase 4 [KO:K00715] [EC:2.4.1.62]
            6483  ST3GAL2; ST3 beta-galactoside alpha-2,3-sialyltransferase 2 [KO:K03368] [EC:2.4.3.2 2.4.3.4]
            6482  ST3GAL1; ST3 beta-galactoside alpha-2,3-sialyltransferase 1 [KO:K00780] [EC:2.4.3.2 2.4.3.4]
            29906  ST8SIA5; ST8 alpha-N-acetyl-neuraminide alpha-2,8-sialyltransferase 5 [KO:K03369] [EC:2.4.3.-]
            8869  ST3GAL5; ST3 beta-galactoside alpha-2,3-sialyltransferase 5 [KO:K03370] [EC:2.4.3.9]
            6489  ST8SIA1; ST8 alpha-N-acetyl-neuraminide alpha-2,8-sialyltransferase 1 [KO:K03371] [EC:2.4.3.8]
            9197  SLC33A1; solute carrier family 33 member 1 [KO:K03372] [EC:2.3.1.-]
            256435  ST6GALNAC3; ST6 N-acetylgalactosaminide alpha-2,6-sialyltransferase 3 [KO:K03373] [EC:2.4.3.7]
            27090  ST6GALNAC4; ST6 N-acetylgalactosaminide alpha-2,6-sialyltransferase 4 [KO:K03374] [EC:2.4.3.7]
            81849  ST6GALNAC5; ST6 N-acetylgalactosaminide alpha-2,6-sialyltransferase 5 [KO:K03375] [EC:2.4.3.-]
            30815  ST6GALNAC6; ST6 N-acetylgalactosaminide alpha-2,6-sialyltransferase 6 [KO:K03376] [EC:2.4.3.-]
            2720  GLB1; galactosidase beta 1 [KO:K12309] [EC:3.2.1.23]
            3073  HEXA; hexosaminidase subunit alpha [KO:K12373] [EC:3.2.1.52]
            3074  HEXB; hexosaminidase subunit beta [KO:K12373] [EC:3.2.1.52]
COMPOUND    G00092  Lactosylceramide
            G00108  GM3
            G00109  GM2
            G00110  GM1
            G00111  GD1a
            G00112  GT1a
            G00113  GD3
            G00114  GD2
            G00115  GD1b
            G00116  GT1b
            G00117  GQ1b
            G00118  GT3
            G00119  GT2
            G00120  GT1c
            G00121  GQ1c
            G00122  GP1c
            G00123  GA2
            G00124  GA1
            G00125  GM1b
            G00126  GD1c
            G00127  GD1a
            G00128  GT1aalpha
            G00129  GQ1balpha
            G00130  GM2alpha
            G00131  GM1alpha
            G00132  GD1beta
            G00166  Fucosyl-GM1
            G00167  N-Acetylgalactosaminyl GM1b
            G00168  N-Acetylgalactosaminyl GD1a
            G00169  9-O-Acetylated GD3
            G00170  9-O-Acetylated GT3
REL_PATHWAY hsa00600  Sphingolipid metabolism
KO_PATHWAY  ko00604
///
