ENTRY       hsa00601                    Pathway
NAME        Glycosphingolipid biosynthesis - lacto and neolacto series - Homo sapiens (human)
CLASS       Metabolism; Glycan biosynthesis and metabolism
PATHWAY_MAP hsa00601  Glycosphingolipid biosynthesis - lacto and neolacto series
MODULE      hsa_M00070  Glycosphingolipid biosynthesis, lacto-series, LacCer => Lc4Cer [PATH:hsa00601]
            hsa_M00071  Glycosphingolipid biosynthesis, neolacto-series, LacCer => nLc4Cer [PATH:hsa00601]
DBLINKS     GO: 0001572
ORGANISM    Homo sapiens (human) [GN:hsa]
GENE        84002  B3GNT5; UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 5 [KO:K03766] [EC:2.4.1.206]
            8708  B3GALT1; beta-1,3-galactosyltransferase 1 [KO:K07819] [EC:2.4.1.86]
            8707  B3GALT2; beta-1,3-galactosyltransferase 2 [KO:K07820] [EC:2.4.1.86]
            10317  B3GALT5; beta-1,3-galactosyltransferase 5 [KO:K03877] [EC:2.4.1.-]
            2523  FUT1; fucosyltransferase 1 (H blood group) [KO:K00718] [EC:2.4.1.69]
            2524  FUT2; fucosyltransferase 2 [KO:K00718] [EC:2.4.1.69]
            2525  FUT3; fucosyltransferase 3 (Lewis blood group) [KO:K00716] [EC:2.4.1.65]
            6487  ST3GAL3; ST3 beta-galactoside alpha-2,3-sialyltransferase 3 [KO:K00781] [EC:2.4.3.6]
            6484  ST3GAL4; ST3 beta-galactoside alpha-2,3-sialyltransferase 4 [KO:K03494] [EC:2.4.3.2 2.4.3.4 2.4.3.6]
            28  ABO; ABO, alpha 1-3-N-acetylgalactosaminyltransferase and alpha 1-3-galactosyltransferase [KO:K00709] [EC:2.4.1.40 2.4.1.37]
            2683  B4GALT1; beta-1,4-galactosyltransferase 1 [KO:K07966] [EC:2.4.1.22 2.4.1.90 2.4.1.38 2.4.1.-]
            8704  B4GALT2; beta-1,4-galactosyltransferase 2 [KO:K07967] [EC:2.4.1.22 2.4.1.90 2.4.1.38 2.4.1.-]
            8703  B4GALT3; beta-1,4-galactosyltransferase 3 [KO:K07968] [EC:2.4.1.90 2.4.1.38 2.4.1.-]
            8702  B4GALT4; beta-1,4-galactosyltransferase 4 [KO:K07969] [EC:2.4.1.90 2.4.1.275 2.4.1.-]
            10690  FUT9; fucosyltransferase 9 [KO:K03663] [EC:2.4.1.152]
            2526  FUT4; fucosyltransferase 4 [KO:K07632] [EC:2.4.1.-]
            2527  FUT5; fucosyltransferase 5 [KO:K07633] [EC:2.4.1.65]
            2528  FUT6; fucosyltransferase 6 [KO:K07634] [EC:2.4.1.65]
            2529  FUT7; fucosyltransferase 7 [KO:K07635] [EC:2.4.1.-]
            10402  ST3GAL6; ST3 beta-galactoside alpha-2,3-sialyltransferase 6 [KO:K03792] [EC:2.4.3.6]
            6489  ST8SIA1; ST8 alpha-N-acetyl-neuraminide alpha-2,8-sialyltransferase 1 [KO:K03371] [EC:2.4.3.8]
            53947  A4GALT; alpha 1,4-galactosyltransferase (P blood group) [KO:K01988] [EC:2.4.1.228]
            8706  B3GALNT1; beta-1,3-N-acetylgalactosaminyltransferase 1 (globoside blood group) [KO:K00719] [EC:2.4.1.79]
            10678  B3GNT2; UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 2 [KO:K00741] [EC:2.4.1.149]
            10331  B3GNT3; UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 3 [KO:K07970] [EC:2.4.1.146 2.4.1.149]
            79369  B3GNT4; UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase 4 [KO:K07971] [EC:2.4.1.149]
            2651  GCNT2; glucosaminyl (N-acetyl) transferase 2 (I blood group) [KO:K00742] [EC:2.4.1.150]
COMPOUND    G00036  Lc3Cer
            G00037  Lc4Cer
            G00038
            G00039  Type IB glycolipid
            G00040
            G00042  Type IA glycolipid
            G00043
            G00044  IV2Fuc-Lc4Cer
            G00045  IV2Fuc,III4Fuc-Lc4Cer
            G00046  Fuc-Lc4Cer
            G00047  3'-isoLM1
            G00048  Fuc-3'-isoLM1
            G00050  Paragloboside
            G00051  nLc5Cer
            G00052  Type II B antigen
            G00054  Type II A antigen
            G00055  IV2Fuc-nLc4Cer
            G00056  III3,IV2Fuc-nLc4Cer
            G00057
            G00058  Type IIIH glycolipid
            G00059  Type IIIA glycolipid
            G00060  III3Fuc-nLc4Cer
            G00061  Sialyl-6-paragloboside
            G00062  Sialyl-3-paragloboside
            G00063  IV3NeuAc,III3Fuc-nLc4Cer
            G00064  3',8'-LD1
            G00066  nLc5Cer
            G00067  nLc6Cer
            G00068  nLc7Cer
            G00069  nLc8Cer
            G00071  VI2Fuc-nLc6
            G00072
            G00073
            G00074
            G00075  Type IIIAb
            G00076  III3Fuc-nLc6Cer
            G00077
            G00078  iso-nLc8Cer
            G00079
            G00080
            G00081
            G00082
            G00083
            G00084
            G00085
            G00086
            G00087  VI6NeuAc-nLc6Cer
            G00088  VI3NeuAc-nLc6Cer
            G00089  V3Fuc-nLc6Cer
            G00090  V3Fuc,III3Fuc-nLc6Cer
            G00091
            G00092  Lactosylceramide
            G00428  IV4Gala-nLc4-Cer
            G00889  PX2
REL_PATHWAY hsa00600  Sphingolipid metabolism
KO_PATHWAY  ko00601
///
