ENTRY       hsa00500                    Pathway
NAME        Starch and sucrose metabolism - Homo sapiens (human)
CLASS       Metabolism; Carbohydrate metabolism
PATHWAY_MAP hsa00500  Starch and sucrose metabolism
MODULE      hsa_M00854  Glycogen biosynthesis, glucose-1P => glycogen/starch [PATH:hsa00500]
            hsa_M00855  Glycogen degradation, glycogen => glucose-6P [PATH:hsa00500]
NETWORK     nt06017  Glycogen metabolism
  ELEMENT   N00713  Glycogen biosynthesis
            N00718  Glycogen degradation
            N00720  Glycogen degradation (amylase)
DRUG        D00216  Acarbose (JAN/USAN/INN)
            D00625  Miglitol (JP18/USAN/INN)
            D01665  Voglibose (JP18/USAN/INN)
            D03342  Camiglibose (USAN)
            D04537  Ingliforib (USAN/INN)
            D09605  Duvoglustat (USAN/INN)
            D09606  Duvoglustat hydrochloride (USAN)
            D11744  Avalglucosidase alfa (USAN/INN)
            D11798  Cipaglucosidase alfa (USAN)
            D11828  Clervonafusp alfa (USAN/INN)
DBLINKS     GO: 0005982 0005985
ORGANISM    Homo sapiens (human) [GN:hsa]
GENE        8972  MGAM; maltase-glucoamylase [KO:K12047] [EC:3.2.1.20 3.2.1.3]
            93432  MGAM2; maltase-glucoamylase 2 (putative) [KO:K12047] [EC:3.2.1.20 3.2.1.3]
            2548  GAA; alpha glucosidase [KO:K12316] [EC:3.2.1.20]
            2595  GANC; glucosidase alpha, neutral C [KO:K12317] [EC:3.2.1.20]
            6476  SI; sucrase-isomaltase [KO:K01203] [EC:3.2.1.48 3.2.1.10]
            7360  UGP2; UDP-glucose pyrophosphorylase 2 [KO:K00963] [EC:2.7.7.9]
            5167  ENPP1; ectonucleotide pyrophosphatase/phosphodiesterase 1 [KO:K01513] [EC:3.1.4.1 3.6.1.9]
            5169  ENPP3; ectonucleotide pyrophosphatase/phosphodiesterase 3 [KO:K01513] [EC:3.1.4.1 3.6.1.9]
            57733  GBA3; glucosylceramidase beta 3 (gene/pseudogene) [KO:K05350] [EC:3.2.1.21]
            2998  GYS2; glycogen synthase 2 [KO:K00693] [EC:2.4.1.11]
            2997  GYS1; glycogen synthase 1 [KO:K00693] [EC:2.4.1.11]
            2992  GYG1; glycogenin 1 [KO:K00750] [EC:2.4.1.186]
            8908  GYG2; glycogenin 2 [KO:K00750] [EC:2.4.1.186]
            2632  GBE1; 1,4-alpha-glucan branching enzyme 1 [KO:K00700] [EC:2.4.1.18]
            5836  PYGL; glycogen phosphorylase L [KO:K00688] [EC:2.4.1.1]
            5837  PYGM; glycogen phosphorylase, muscle associated [KO:K00688] [EC:2.4.1.1]
            5834  PYGB; glycogen phosphorylase B [KO:K00688] [EC:2.4.1.1]
            178  AGL; amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase [KO:K01196] [EC:2.4.1.25 3.2.1.33]
            278  AMY1C; amylase alpha 1C [KO:K01176] [EC:3.2.1.1]
            279  AMY2A; amylase alpha 2A [KO:K01176] [EC:3.2.1.1]
            276  AMY1A; amylase alpha 1A [KO:K01176] [EC:3.2.1.1]
            280  AMY2B; amylase alpha 2B [KO:K01176] [EC:3.2.1.1]
            277  AMY1B; amylase alpha 1B [KO:K01176] [EC:3.2.1.1]
            11181  TREH; trehalase [KO:K01194] [EC:3.2.1.28]
            5236  PGM1; phosphoglucomutase 1 [KO:K01835] [EC:5.4.2.2]
            55276  PGM2; phosphoglucomutase 2 [KO:K15779] [EC:5.4.2.2 5.4.2.7]
            3101  HK3; hexokinase 3 [KO:K00844] [EC:2.7.1.1]
            3098  HK1; hexokinase 1 [KO:K00844] [EC:2.7.1.1]
            3099  HK2; hexokinase 2 [KO:K00844] [EC:2.7.1.1]
            80201  HKDC1; hexokinase domain containing 1 [KO:K00844] [EC:2.7.1.1]
            2645  GCK; glucokinase [KO:K12407] [EC:2.7.1.2]
            2538  G6PC1; glucose-6-phosphatase catalytic subunit 1 [KO:K01084] [EC:3.1.3.9]
            57818  G6PC2; glucose-6-phosphatase catalytic subunit 2 [KO:K01084] [EC:3.1.3.9]
            92579  G6PC3; glucose-6-phosphatase catalytic subunit 3 [KO:K01084] [EC:3.1.3.9]
            283209  PGM2L1; phosphoglucomutase 2 like 1 [KO:K11809] [EC:2.7.1.106]
            2821  GPI; glucose-6-phosphate isomerase [KO:K01810] [EC:5.3.1.9]
COMPOUND    C00029  UDP-glucose
            C00031  D-Glucose
            C00085  D-Fructose 6-phosphate
            C00089  Sucrose
            C00092  D-Glucose 6-phosphate
            C00095  D-Fructose
            C00103  D-Glucose 1-phosphate
            C00185  Cellobiose
            C00208  Maltose
            C00252  Isomaltose
            C00369  Starch
            C00372  Dextran
            C00394  GDP-glucose
            C00498  ADP-glucose
            C00501  CDP-glucose
            C00663  beta-D-Glucose 1-phosphate
            C00689  alpha,alpha'-Trehalose 6-phosphate
            C00718  Amylose
            C00721  Dextrin
            C00760  Cellulose
            C00963  beta-D-Glucoside
            C00965  1,3-beta-D-Glucan
            C00973  Cyclomaltodextrin
            C01083  alpha,alpha-Trehalose
            C01231  alpha-D-Glucose 1,6-bisphosphate
            C01725  Levanbiose
            C01898  Cellodextrin
            C01935  Maltodextrin
            C02591  Sucrose 6'-phosphate
            C02995  Maltose 6'-phosphate
            C03323  (2,1-beta-D-Fructosyl)n
            C04534  6-Phospho-beta-D-glucosyl-(1,4)-D-glucose
            C05731  3-Ketosucrose
            C06215  Levan
            C06400  1-alpha-D-[(1->4)-alpha-D-Glucosyl](n-1)-alpha-D-glucopyranoside
            C16688  Sucrose 6-phosphate
            C20237  alpha-Maltose 1-phosphate
REL_PATHWAY hsa00010  Glycolysis / Gluconeogenesis
            hsa00520  Amino sugar and nucleotide sugar metabolism
KO_PATHWAY  ko00500
///
