ENTRY       hsa00410                    Pathway
NAME        beta-Alanine metabolism - Homo sapiens (human)
CLASS       Metabolism; Metabolism of other amino acids
PATHWAY_MAP hsa00410  beta-Alanine metabolism
DBLINKS     GO: 0019482
ORGANISM    Homo sapiens (human) [GN:hsa]
GENE        339896  GADL1; glutamate decarboxylase like 1 [KO:K18966] [EC:4.1.1.29 4.1.1.11]
            51380  CSAD; cysteine sulfinic acid decarboxylase [KO:K18966] [EC:4.1.1.29 4.1.1.11]
            2571  GAD1; glutamate decarboxylase 1 [KO:K01580] [EC:4.1.1.15]
            2572  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
            84735  CNDP1; carnosine dipeptidase 1 [KO:K05604] [EC:3.4.13.20]
            57571  CARNS1; carnosine synthase 1 [KO:K14755] [EC:6.3.2.11]
            55748  CNDP2; carnosine dipeptidase 2 [KO:K08660] [EC:3.4.13.18]
            18  ABAT; 4-aminobutyrate aminotransferase [KO:K13524] [EC:2.6.1.19 2.6.1.22]
            54498  SMOX; spermine oxidase [KO:K12259] [EC:1.5.3.16 1.5.3.-]
            8639  AOC3; amine oxidase copper containing 3 [KO:K00276] [EC:1.4.3.21]
            314  AOC2; amine oxidase copper containing 2 [KO:K00276] [EC:1.4.3.21]
            217  ALDH2; aldehyde dehydrogenase 2 family member [KO:K00128] [EC:1.2.1.3]
            224  ALDH3A2; aldehyde dehydrogenase 3 family member A2 [KO:K00128] [EC:1.2.1.3]
            219  ALDH1B1; aldehyde dehydrogenase 1 family member B1 [KO:K00128] [EC:1.2.1.3]
            501  ALDH7A1; aldehyde dehydrogenase 7 family member A1 [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
            223  ALDH9A1; aldehyde dehydrogenase 9 family member A1 [KO:K00149] [EC:1.2.1.47 1.2.1.3]
            221  ALDH3B1; aldehyde dehydrogenase 3 family member B1 [KO:K00129] [EC:1.2.1.5]
            222  ALDH3B2; aldehyde dehydrogenase 3 family member B2 [KO:K00129] [EC:1.2.1.5]
            218  ALDH3A1; aldehyde dehydrogenase 3 family member A1 [KO:K00129] [EC:1.2.1.5]
            1806  DPYD; dihydropyrimidine dehydrogenase [KO:K00207] [EC:1.3.1.2]
            1807  DPYS; dihydropyrimidinase [KO:K01464] [EC:3.5.2.2]
            51733  UPB1; beta-ureidopropionase 1 [KO:K01431] [EC:3.5.1.6]
            26275  HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [KO:K05605] [EC:3.1.2.4]
            3030  HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha [KO:K07515] [EC:4.2.1.17 1.1.1.211]
            1962  EHHADH; enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
            1892  ECHS1; enoyl-CoA hydratase, short chain 1 [KO:K07511] [EC:4.2.1.17]
            35  ACADS; acyl-CoA dehydrogenase short chain [KO:K00248] [EC:1.3.8.1]
            8310  ACOX3; acyl-CoA oxidase 3, pristanoyl [KO:K00232] [EC:1.3.3.6]
            51  ACOX1; acyl-CoA oxidase 1 [KO:K00232] [EC:1.3.3.6]
            23417  MLYCD; malonyl-CoA decarboxylase [KO:K01578] [EC:4.1.1.9]
            4329  ALDH6A1; aldehyde dehydrogenase 6 family member A1 [KO:K00140] [EC:1.2.1.18 1.2.1.27]
COMPOUND    C00024  Acetyl-CoA
            C00049  L-Aspartate
            C00083  Malonyl-CoA
            C00099  beta-Alanine
            C00100  Propanoyl-CoA
            C00106  Uracil
            C00135  L-Histidine
            C00222  3-Oxopropanoate
            C00315  Spermidine
            C00334  4-Aminobutanoate
            C00383  Malonate
            C00386  Carnosine
            C00429  5,6-Dihydrouracil
            C00555  4-Aminobutyraldehyde
            C00750  Spermine
            C00804  Propynoate
            C00864  Pantothenate
            C00894  Propenoyl-CoA
            C00986  1,3-Diaminopropane
            C01013  3-Hydroxypropanoate
            C01073  N-Acetyl-beta-alanine
            C01262  beta-Alanyl-N(pi)-methyl-L-histidine
            C02335  beta-Alanyl-CoA
            C02642  3-Ureidopropionate
            C03492  D-4'-Phosphopantothenate
            C03722  Quinolinate
            C05340  beta-Alanyl-L-arginine
            C05341  beta-Alanyl-L-lysine
            C05665  3-Aminopropanal
            C05668  3-Hydroxypropionyl-CoA
            C05669  beta-Nitropropanoate
            C05670  3-Aminopropiononitrile
REL_PATHWAY hsa00061  Fatty acid biosynthesis
            hsa00240  Pyrimidine metabolism
            hsa00250  Alanine, aspartate and glutamate metabolism
            hsa00330  Arginine and proline metabolism
            hsa00640  Propanoate metabolism
            hsa00770  Pantothenate and CoA biosynthesis
KO_PATHWAY  ko00410
///
