ENTRY       hsa00051                    Pathway
NAME        Fructose and mannose metabolism - Homo sapiens (human)
CLASS       Metabolism; Carbohydrate metabolism
PATHWAY_MAP hsa00051  Fructose and mannose metabolism
DRUG        D01688  Epalrestat (JP18/INN)
            D01715  Risarestat (INN)
            D01842  Fidarestat (JAN/INN)
            D02323  Tolrestat (USAN/INN)
            D02328  Zopolrestat (USAN/INN)
            D02835  Alrestatin sodium (USAN)
            D03803  Lidorestat (USAN)
            D03805  Minalrestat (USAN/INN)
            D03806  Ponalrestat (USAN/INN)
            D03807  Zenarestat (USAN/INN)
            D05893  Sorbinil (USAN/INN)
            D06403  Ranirestat (JAN/INN)
            D12384  Govorestat (USAN/INN)
            D12390  Caficrestat (USAN/INN)
DBLINKS     GO: 0006000 0006013
ORGANISM    Homo sapiens (human) [GN:hsa]
GENE        4351  MPI; mannose phosphate isomerase [KO:K01809] [EC:5.3.1.8]
            5373  PMM2; phosphomannomutase 2 [KO:K17497] [EC:5.4.2.8]
            5372  PMM1; phosphomannomutase 1 [KO:K17497] [EC:5.4.2.8]
            29925  GMPPB; GDP-mannose pyrophosphorylase B [KO:K00966] [EC:2.7.7.13]
            29926  GMPPA; GDP-mannose pyrophosphorylase A [KO:K00966] [EC:2.7.7.13]
            2762  GMDS; GDP-mannose 4,6-dehydratase [KO:K01711] [EC:4.2.1.47]
            7264  GFUS; GDP-L-fucose synthase [KO:K02377] [EC:1.1.1.271]
            8790  FPGT; fucose-1-phosphate guanylyltransferase [KO:K00976] [EC:2.7.7.30]
            197258  FCSK; fucose kinase [KO:K05305] [EC:2.7.1.52]
            55556  ENOSF1; enolase superfamily member 1 [KO:K18334] [EC:4.2.1.68]
            3101  HK3; hexokinase 3 [KO:K00844] [EC:2.7.1.1]
            3098  HK1; hexokinase 1 [KO:K00844] [EC:2.7.1.1]
            3099  HK2; hexokinase 2 [KO:K00844] [EC:2.7.1.1]
            80201  HKDC1; hexokinase domain containing 1 [KO:K00844] [EC:2.7.1.1]
            5213  PFKM; phosphofructokinase, muscle [KO:K00850] [EC:2.7.1.11]
            5214  PFKP; phosphofructokinase, platelet [KO:K00850] [EC:2.7.1.11]
            5211  PFKL; phosphofructokinase, liver type [KO:K00850] [EC:2.7.1.11]
            2203  FBP1; fructose-bisphosphatase 1 [KO:K03841] [EC:3.1.3.11]
            8789  FBP2; fructose-bisphosphatase 2 [KO:K03841] [EC:3.1.3.11]
            5207  PFKFB1; 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 1 [KO:K19028] [EC:2.7.1.105 3.1.3.46]
            5208  PFKFB2; 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 2 [KO:K19029] [EC:2.7.1.105 3.1.3.46]
            5209  PFKFB3; 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 3 [KO:K01103] [EC:2.7.1.105 3.1.3.46]
            5210  PFKFB4; 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 4 [KO:K19030] [EC:2.7.1.105 3.1.3.46]
            57103  TIGAR; TP53 induced glycolysis regulatory phosphatase [KO:K14634] [EC:3.1.3.46]
            3795  KHK; ketohexokinase [KO:K00846] [EC:2.7.1.3]
            6652  SORD; sorbitol dehydrogenase [KO:K00008] [EC:1.1.1.14]
            231  AKR1B1; aldo-keto reductase family 1 member B [KO:K00011] [EC:1.1.1.21]
            57016  AKR1B10; aldo-keto reductase family 1 member B10 [KO:K00011] [EC:1.1.1.21]
            230  ALDOC; aldolase, fructose-bisphosphate C [KO:K01623] [EC:4.1.2.13]
            226  ALDOA; aldolase, fructose-bisphosphate A [KO:K01623] [EC:4.1.2.13]
            229  ALDOB; aldolase, fructose-bisphosphate B [KO:K01623] [EC:4.1.2.13]
            7167  TPI1; triosephosphate isomerase 1 [KO:K01803] [EC:5.3.1.1]
            26007  TKFC; triokinase and FMN cyclase [KO:K00863] [EC:2.7.1.28 2.7.1.29 4.6.1.15]
COMPOUND    C00095  D-Fructose
            C00096  GDP-mannose
            C00111  Glycerone phosphate
            C00118  D-Glyceraldehyde 3-phosphate
            C00159  D-Mannose
            C00186  (S)-Lactate
            C00247  L-Sorbose
            C00267  alpha-D-Glucose
            C00275  D-Mannose 6-phosphate
            C00325  GDP-L-fucose
            C00392  Mannitol
            C00424  (S)-Lactaldehyde
            C00464  Mannan
            C00507  L-Rhamnose
            C00577  D-Glyceraldehyde
            C00636  D-Mannose 1-phosphate
            C00644  D-Mannitol 1-phosphate
            C00665  beta-D-Fructose 2,6-bisphosphate
            C00794  D-Sorbitol
            C00861  L-Rhamnulose
            C00976  GDP-D-mannuronate
            C01019  L-Fucose
            C01094  D-Fructose 1-phosphate
            C01096  Sorbitol 6-phosphate
            C01099  L-Fuculose 1-phosphate
            C01131  L-Rhamnulose 1-phosphate
            C01222  GDP-4-dehydro-6-deoxy-D-mannose
            C01355  Fructan
            C01487  D-Allose
            C01720  L-Fuconate
            C01721  L-Fuculose
            C01768  (Alginate)n
            C01934  L-Rhamnonate
            C02431  L-Rhamnofuranose
            C02492  1,4-beta-D-Mannan
            C02888  Sorbose 1-phosphate
            C02962  D-Allose 6-phosphate
            C02977  GDP-6-deoxy-D-talose
            C02985  L-Fucose 1-phosphate
            C02991  L-Rhamnono-1,4-lactone
            C03117  GDP-6-deoxy-D-mannose
            C03267  beta-D-Fructose 2-phosphate
            C03827  2-Dehydro-3-deoxy-L-fuconate
            C03979  2-Dehydro-3-deoxy-L-rhamnonate
            C05144  (beta-D-Mannuronate)n
            C05345  beta-D-Fructose 6-phosphate
            C05378  beta-D-Fructose 1,6-bisphosphate
            C05392  Oligouronide with 4-deoxy-alpha-L-erythro-hex-4-enopyranuronosyl group
            C06192  ADP-mannose
            C11516  2-(alpha-D-Mannosyl)-3-phosphoglycerate
            C11544  2-O-(alpha-D-Mannosyl)-D-glycerate
            C18028  L-Fucono-1,5-lactone
            C18096  D-Allulose 6-phosphate
            C20781  2,4-Diketo-3-deoxy-L-fuconate
REL_PATHWAY hsa00010  Glycolysis / Gluconeogenesis
            hsa00052  Galactose metabolism
            hsa00053  Ascorbate and aldarate metabolism
            hsa00510  N-Glycan biosynthesis
            hsa00520  Amino sugar and nucleotide sugar metabolism
            hsa00620  Pyruvate metabolism
KO_PATHWAY  ko00051
///
