The third brother, 42 years old, diagnosed with VHL also presents a right pheochromocytoma already treated and renal clear cell tumors already excised.
A temporary exploration revealed a temporalmaurosis of the right eye after suffering a tractional RD, with cataract that prevented its visualization, and in the left eye a whitish exudation in the form of a large papillokin
Angiography showed a large papillary angioma of its diameter with high hyperfluorescence, as well as superior HCR.
OCT showed intraretinal edema near the papilla without affecting the macula, with a VA of 0.8.
She is being treated with intravitreal injections of beizumab.
