A 3-month-old girl with an erythematous lesion on her face, small round plaques, slightly atrophic in the bilateral temporo-occipital region and neck and telangiectasias on her surface.
In the genital region, erythematous, atrophic lesion with defined edges of 2 months of evolution.
1.
She presented scar alopecia, dry eye, dry mouth and anemia, without a diagnosis of her disease at the time of consultation.
Homogeneous anti-patient pattern: Hb 11.2g/L, Hto 33%, GDT 265 IU/L, GPT 212 IU/L, FAL 927 IU/L, C3 54 mg/dl,
Histopathological study: thickened corneal layer, thinned epidermis, intense vacuolization of basal keratinocytes in dermis diffuse mononuclear infiltrate.
Target tissues
DIF negative.
1.
Cardiological evaluation was normal.
Treatment: topical hydrolytic agents 1%, Pimecrolimus 1%.
Erythematous lesions disappeared within 15 days and atrophic lesions persisted with petechial scalp punctate, normalizing liver enzymes at 10 months of life.
The mother was then diagnosed with Sjögren's Syndrome (Sme.).
