A 32-year-old man from North Shewa, Central part of Ethiopia, presented to Menelik II Hospital in June 2019 with chief compliant of reduction of vision of 2 year duration. The reduction of vision had been since childhood but worsened in the past 2 years. The low vision was worse at distance and he has learned that his eyes were large since childhood. Family history was unremarkable and there was no consanguinity of the parents. Physical examination showed that best corrected visual acuity (BCVA) of counting finger at one and three meters in the right and left eyes respectively. Average repeated IOP measured by I- care tonometer was 12 mmHg for right eye and 11 mmHg in the left eye. Pupils were equal in size and reactive to light, there was no relative afferent pupillary defect. Horizontal corneal diameter was 14mm () in both eyes with stromal opacities and Haab's striae (). Anterior chambers were deep and gonioscopy revealed wide open angles in both eyes. There was iridodonesis, phacodonesis, as well as superiorly and nasally subluxated cataract lenses in both eyes. The cataract in the right eye was denser. Optic nerve head evaluation by 90D lens showed pink rim with vertical cup- to- disc ratio of 0.6 in both eyes with no nerve fiber layer loss (). Visual field examination was normal in both eyes (right eye examination was done after cataract surgery). Central corneal thickness was 466um in the right eye and 467um for the left eye. Axial length was 30.3mm and 29.9mm for right and left eyes respectively. The diagnosis of subluxated cataract of both eyes, but denser on right and spontaneously arrested primary congenital glaucoma was reached. After counseling and discussion on prognosis with the patient, manual small incision cataract surgery was done for the right eye. On 2nd post-operative week, the right eye BCVA was 6/36 and poor vision was explained by amblyopia. After one month the IOP was normal, but intraocular lens (IOL) was dislocated and BCVA decreased to 6/60.