A 44-year-old woman presented with progressive kyphosis for more than 10 years and low back pain in the past 2 years. It had been about 10 years since she suffered from kyphosis, just after she gave birth. After long standing and fatigue, she began to feel low back pain, and her height became shorter after getting up in the morning, but she had not been diagnosed and treated. She suffered from severe inferiority due to deformity as well. In the last 2 years, her pain was gradually aggravated. Neurofibromatosis was diagnosed at a local hospital many years ago. The patient had no previous medical history. The patient was 144 cm in height and had a weight of 40 kg. A mass of café-au-lait spots and neurofibromas can be found over her body. She presented thoracolumbar angular kyphosis, but no spinal cord damage or neurological dysfunction. The bone mineral density is as follows: Femoral neck, 0.747 g/cm2; and T-score: -1.8. The bone mass of the femur decreased. Preoperative computerized tomography (CT) and magnetic resonance imaging examinations showed rotatory subluxation of L2 vertebra, spontaneous fusion of T12-L4 vertebrae, thin pedicles of L1-L5, expansion of dural ectasia, and spinal cord located in the concave side (right).